نتایج جستجو برای: autozygosity

تعداد نتایج: 143  

2014
Arundhati Dev Borman Laura R Pearce Donna S Mackay Kerstin Nagel-Wolfrum Alice E Davidson Robert Henderson Sumedha Garg Naushin H Waseem Andrew R Webster Vincent Plagnol Uwe Wolfrum I Sadaf Farooqi Anthony T Moore

Inherited retinal dystrophies are a major cause of childhood blindness. Here, we describe the identification of a homozygous frameshift mutation (c.1194_1195delAG, p.Arg398Serfs*9) in TUB in a child from a consanguineous UK Caucasian family investigated using autozygosity mapping and whole-exome sequencing. The proband presented with obesity, night blindness, decreased visual acuity, and electr...

2012
Erik G. Puffenberger Robert N. Jinks Carrie Sougnez Kristian Cibulskis Rebecca A. Willert Nathan P. Achilly Ryan P. Cassidy Christopher J. Fiorentini Kory F. Heiken Johnny J. Lawrence Molly H. Mahoney Christopher J. Miller Devika T. Nair Kristin A. Politi Kimberly N. Worcester Roni A. Setton Rosa DiPiazza Eric A. Sherman James T. Eastman Christopher Francklyn Susan Robey-Bond Nicholas L. Rider Stacey Gabriel D. Holmes Morton Kevin A. Strauss

The Clinic for Special Children (CSC) has integrated biochemical and molecular methods into a rural pediatric practice serving Old Order Amish and Mennonite (Plain) children. Among the Plain people, we have used single nucleotide polymorphism (SNP) microarrays to genetically map recessive disorders to large autozygous haplotype blocks (mean = 4.4 Mb) that contain many genes (mean = 79). For som...

2017
Mohammadreza Dehghani Masoud Dehghan Tezerjani Zahra Metanat Mohammad Yahya Vahidi Mehrjardi

Anophthalmia or microphthalmia (A/M) is a rare group of congenital/developmental ocular malformations, characterized by absent or small eye within the orbit affecting one or both eyes. It has complex etiology with chromosomal, monogenic with high heterogeneity, and environmental causes. We performed genome SNP-array analysis followed by autozygosity mapping and sequencing in the members of two ...

Anophthalmia or microphthalmia (A/M) is a rare group of congenital/developmental ocular malformations, characterized by absent or small eye within the orbit affecting one or both eyes. It  has complex etiology with chromosomal, monogenic with high heterogeneity, and environmental causes. We performed genome SNP-array analysis followed by autozygosity mapping and sequencing in the members o...

Journal: :genetics in the 3rd millennium 0
تارا اخترخاوری tara akhtarkhavari مژگان بابا نژاد mojgan babanejad مرضیه محسنی marzieh mohseni خدیجه جلالوند khadijeh jalalvand حسین نجم آبادی hossein najmabadi کیمیا کهریزی kimia kahrizi

heredity hearing loss (hl) is the most prevalent sensory disorder and most cases are non-syndromic. eighty percent of non-syndromic sensorineural deaf patients show an autosomal recessive pattern of inheritance. to date, 47 genes and 98 loci have been reported for this mode of inheritance. previous studies in our center showed the high prevalence of dfnb3 among iranian deaf families. pjvk (dfnb...

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