نتایج جستجو برای: alps

تعداد نتایج: 5744  

2013
Monique Genest James Sturgis Guillaume Drin Julie Ménétrey Germain Trugnan Paula González-Rubio Garrido

The research about membrane-shape related processes is a new fascinating field. Recently an increasing number of lipid-binding domains that sculpt or sense the shape of the membrane have been identified. Most of the studies about membrane-shape have been focus on the generation of the curvature and less attention has been put on the mechanism of curvature sensing. Thus, this fascinating subject...

2015
V. Koneti Rao

Autoimmune lymphoproliferative syndrome (ALPS) is a rare disorder of apoptosis. It is frequently caused by mutations in FAS (TNFRSF6) gene. Unlike most of the self-limiting autoimmune cytopenias sporadically seen in childhood, multi lineage cytopenias due to ALPS are often refractory, as their inherited genetic defect is not going to go away. Historically, more ALPS patients have died due to ov...

Journal: :Clinical and vaccine immunology : CVI 2015
Johan A Maeland Jan E Afset Randi V Lyng Andreas Radtke

Nearly all Streptococcus agalactiae (group B streptococcus [GBS]) strains express a protein which belongs to the so-called alpha-like proteins (Alps), of which Cα, Alp1, Alp2, Alp3, Rib, and Alp4 are known to occur in GBS. The Alps are chimeras which form mosaic structures on the GBS surface. Both N- and C-terminal stretches of the Alps possess immunogenic sites of dissimilar immunological spec...

Journal: :Blood 2014
Bénédicte Neven Julie Bruneau Marie-Claude Stolzenberg Isabelle Meyts Aude Magerus-Chatinet Leen Moens Nina Lanzarotti Sandra Weller Denise Amiranoff Benoit Florkin Brigitte Bader-Meunier Guy Leverger Alice Ferster Christophe Chantrain Stéphane Blanche Capucine Picard Thierry Jo Molina Nicole Brousse Anne Durandy Marta Rizzi Xavier Bossuyt Alain Fischer Frederic Rieux-Laucat

Autoimmune lymphoproliferative syndrome (ALPS) caused by impaired FAS-mediated apoptosis of lymphocytes is characterized by lymphoproliferation, autoimmunity, but also an increased risk of invasive bacterial infection, notably following splenectomy. We surveyed a cohort of 100 ALPS patients (including 33 splenectomized) and found that 12 (10 splenectomized) had experienced 23 invasive bacterial...

Journal: :Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas 2008
J Fernandes R Amorim I Azevedo M J Martins

Our objective was to characterize the modulation of the activity of Saccharomyces cerevisiae alkaline phosphatases (ALPs) by classic inhibitors of ALP activity, cholesterol and steroid hormones, in order to identify catalytic similarities between yeast and mammalian ALPs. S. cerevisiae expresses two ALPs, coded for by the PHO8 and PHO13 genes. The product of the PHO8 gene is repressible by Pi i...

2013
Maurizio Aricò Matteo Melensi Ugo Ramenghi Umberto Dianzani Annalisa Chiocchetti

This article presents a case report for a child presenting with mixed clinical features of autoimmune lymphoproliferative syndrome (ALPS), familial hemophagocytic lymphohistiocytosis (FHL), and X-linked lymphoproliferative (XLP) disease. From 6 months, he exhibited splenomegaly and lymphoadenopathy and from 4 years, he showed recurrent severe autoimmune hemocytopenia and sepsislike bouts of fev...

Journal: :Blood 2014
Susan Price Pamela A Shaw Amy Seitz Gyan Joshi Joie Davis Julie E Niemela Katie Perkins Ronald L Hornung Les Folio Philip S Rosenberg Jennifer M Puck Amy P Hsu Bernice Lo Stefania Pittaluga Elaine S Jaffe Thomas A Fleisher V Koneti Rao Michael J Lenardo

Autoimmune lymphoproliferative syndrome (ALPS) presents in childhood with nonmalignant lymphadenopathy and splenomegaly associated with a characteristic expansion of mature CD4 and CD8 negative or double negative T-cell receptor αβ(+) T lymphocytes. Patients often present with chronic multilineage cytopenias due to autoimmune peripheral destruction and/or splenic sequestration of blood cells an...

Journal: :Computer Networks 2012
Adrian Holzer Patrick Th. Eugster Benoît Garbinato

Location-based publish/subscribe (LPS) is an important building block for contextaware applications in mobile ad hoc networks (MANETs). In LPS, published messages are routed based on their content as well as on the location of publishers and subscribers. Existing LPS algorithms can be coarsely classified as follows: (1) message-centric approaches consist in broadcasting published messages, (2) ...

Journal: :Zootaxa 2014
Erhard Christian Marco Isaia Mauro Paschetta Alexander Bruckner

Current knowledge of the taxonomy and distribution of European cave palpigrades largely rests upon incidental records. Samples seldom comprise more than one or two specimens, and many regions have only been unevenly explored, if at all. The present study is the first to investigate morphological variability within, and differentiation between, subterranean palpigrade populations in a small, geo...

2014
Olivia Charrier Pierre Dupont André Pornon Nathalie Escaravage

Genetic variation within plant species is determined by a number of factors such as reproductive mode, breeding system, life history traits and climatic events. In alpine regions, plants experience heterogenic abiotic conditions that influence the population's genetic structure. The aim of this study was to investigate the genetic structure and phylogeographic history of the subalpine shrub Rho...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید