نتایج جستجو برای: ژن pah

تعداد نتایج: 23292  

2017
David Langleben Stylianos Orfanos

Within the cohort of patients suffering from idiopathic pulmonary arterial hypertension (IPAH) is a group that responds dramatically (VR-PAH) to an acute vasodilator challenge and that has excellent long-term hemodynamic improvement and prognosis on high dose calcium channel blockers compared with vasodilator non-responders (VN-PAH). For the purposes of diagnosing VR-PAH, there is to date no te...

2013
Masataka Kuwana Hiroshi Watanabe Nobushige Matsuoka Naonobu Sugiyama

OBJECTIVES Few studies have focused on pulmonary arterial hypertension (PAH) associated with connective tissue diseases (CTDs). The optimal treatment for CTD-PAH has yet to be established. DESIGN Meta-analysis of the data from evaluations of treatment for PAH generally (19 studies) and CTD-PAH specifically (nine studies) to compare the effects of pulmonary vasodilative PAH agents. MEDLINE, EM...

2009
Paul A. Fowler Peter J. O’Shaughnessy Stewart M. Rhind Jon Ayres

A 140 volume 117 | number 4 | April 2009 • Environmental Health Perspectives PAH Exposure doi:10.1289/ehp.0800445 We were very interested to read the article by Choi et al. (2008). The difference between maternal exposure and our own data on actual concentrations of poly cyclic aromatic hydro carbons (PAHs) in the human male fetal liver (Fowler et al. 2008) was striking. Eight of the PAH exposu...

2017
John Gerry Coghlan Nazzareno Galiè Joan Albert Barberà Adaani E Frost Hossein-Ardeschir Ghofrani Marius M Hoeper Masataka Kuwana Vallerie V McLaughlin Andrew J Peacock Gérald Simonneau Jean-Luc Vachiéry Christiana Blair Hunter Gillies Karen L Miller Julia H N Harris Jonathan Langley Lewis J Rubin

BACKGROUND Patients with connective tissue disease-associated pulmonary arterial hypertension (CTD-PAH), in particular systemic sclerosis (SSc), had an attenuated response compared with idiopathic PAH in most trials. Thus, there is uncertainty regarding the benefit of PAH-targeted therapy in some forms of CTD-PAH. OBJECTIVE To explore the safety and efficacy of initial combination therapy wit...

Journal: :Respiratory care 2010
Ariel M Modrykamien Ravindra Gudavalli Kevin McCarthy Joseph Parambil

BACKGROUND Pulmonary arterial hypertension (PAH) is frequently seen in patients with idiopathic pulmonary fibrosis (IPF). We sought to examine the performance of echocardiography, 6-min walk test (6MWT) distance, distance-saturation product (DSP), and pulse oximetry (SpO2) in detecting underlying PAH in IPF. METHODS 626 lung transplanted patients from February 1990 to December 2007 were consi...

2017
Kathleen Morrisroe Wendy Stevens Joanne Sahhar Candice Rabusa Mandana Nikpour Susanna Proudman Catherine Hill Sue Lester Peter Nash Gian Ngian Mandana Nikpour Susanna Proudman Maureen Rischmueller Janet Roddy Joanne Sahhar Wendy Stevens Gemma Strickland Vivek Thakkar Jenny Walker Jane Zochling

BACKGROUND Pulmonary arterial hypertension (PAH) is the leading cause of death in systemic sclerosis (SSc). Annual screening with echocardiogram (ECHO) is recommended. We present the methodological aspects of a PAH screening programme in a large Australian SSc cohort, the epidemiology of SSc-PAH in this cohort, and an evaluation of factors influencing physician adherence to PAH screening guidel...

Journal: :Clinical and experimental rheumatology 2008
S Chow J E Pope S Mehta

OBJECTIVE Pulmonary arterial hypertension (PAH) affects the quality of life (QoL) and the ability to perform the activities of daily living (ADLs) in patients with systemic sclerosis (SSc). We determined whether the Health Assessment Questionnaire-Disability Index (HAQ-DI), a self-assessment measure of function, correlates with a patient's PAH status in a population of SSc patients with PAH. ...

2013
Yvonne Dempsie Neil A. MacRitchie Kevin White Ian Morecroft Audrey F. Wright Margaret Nilsen Lynn Loughlin Kirsty M. Mair Margaret R. MacLean

AIMS Pulmonary arterial hypertension (PAH) occurs more frequently in women than men. Oestrogen and the oestrogen-metabolising enzyme cytochrome P450 1B1 (CYP1B1) play a role in the development of PAH. Anorectic drugs such as dexfenfluramine (Dfen) have been associated with the development of PAH. Dfen mediates PAH via a serotonergic mechanism and we have shown serotonin to up-regulate expressio...

2014
Charles D. Burger Pamela K. Long Monarch R. Shah Michael D. McGoon Dave P. Miller Alain J. Romero Wade W. Benton Robert E. Safford

BACKGROUND Hospitalization is an important outcome in pulmonary arterial hypertension (PAH), shown previously to correlate with survival. Using the Registry to Evaluate Early and Long-term PAH Disease Management (REVEAL Registry), we sought to characterize first-time hospitalizations and their effect on subsequent hospitalization and survival in patients with newly diagnosed disease. METHODS ...

2016
Su-Jin Yoo Jae-Hyeong Park Yunseon Park Jae-Hwan Lee Byung-Joo Sun Jinhyun Kim In Seol Yoo Seung Cheol Shim Seong Wook Kang

BACKGROUND Pulmonary arterial hypertension (PAH) is a major cause of morbidity and mortality among patients with systemic sclerosis (SSc). Early detection and prompt treatment of PAH associated with SSc (SSc-PAH) result in better prognosis. We conducted echocardiographic study to presume the prevalence of PAH in Korean adult SSc patients and to diagnose SSc-PAH in their early stages with right ...

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