نتایج جستجو برای: polycystic kidney diseases pkd

تعداد نتایج: 1000149  

2014
C. Courivaud C. Roubiou E. Delabrousse C. Bresson-Vautrin J. M. Chalopin D. Ducloux

BACKGROUND For many nephrologists, patients with polycystic kidney disease (PKD) have an increased risk of complications and technique failure on peritoneal dialysis (PD) due to enlarged kidneys. The literature showed that PD can be as good a therapeutic option as haemodialysis (HD) for patients with PKD. However, no study has focused on the impact of polycystic kidney size on outcomes for pati...

Journal: :Journal of the American Society of Nephrology : JASN 2016
Jennifer L Huang Adrian S Woolf Maria Kolatsi-Joannou Peter Baluk Richard N Sandford Dorien J M Peters Donald M McDonald Karen L Price Paul J D Winyard David A Long

Polycystic kidney diseases (PKD) are genetic disorders characterized by progressive epithelial cyst growth leading to destruction of normally functioning renal tissue. Current therapies have focused on the cyst epithelium, and little is known about how the blood and lymphatic microvasculature modulates cystogenesis. Hypomorphic Pkd1(nl/nl) mice were examined, showing that cystogenesis was assoc...

Journal: :Molecular biology of the cell 2006
Jinghua Hu Young-Kyung Bae Karla M Knobel Maureen M Barr

Cilia serve as sensory devices in a diversity of organisms and their defects contribute to many human diseases. In primary cilia of kidney cells, the transient receptor potential polycystin (TRPP) channels polycystin-1 (PC-1) and polycystin-2 (PC-2) act as a mechanosensitive channel, with defects resulting in autosomal dominant polycystic kidney disease. In sensory cilia of Caenorhabditis elega...

Journal: :Drug discovery today. Disease mechanisms 2013
Thomas Weimbs Jeffrey J Talbot

Mutations in the gene coding for the integral membrane protein polycystin-1 (PC1) are the cause of most cases of autosomal-dominant polycystic kidney disease (ADPKD), a very common disease that leads to kidney failure and currently lacks approved treatment. Recent work has revealed that PC1 can regulate the transcription factor STAT3, and that STAT3 is aberrantly activated in the kidneys of ADP...

2017
Hyo Sang Jo Won Sik Eum Eun Young Park Je Young Ko Do Yeon Kim Dae Won Kim Min Jea Shin Ora Son Su Bin Cho Jung Hwan Park Chi Hern Lee Eun Ji Yeo Hyeon Ji Yeo Yeon Joo Choi Jong Kyu Youn Sung-Woo Cho Jinseu Park Jong Hoon Park Soo Young Choi

Polycystic kidney disease (PKD) is one of the most common inherited disorders, involving progressive cyst formation in the kidney that leads to renal failure. FK506 binding protein 12 (FK506BP) is an immunophilin protein that performs multiple functions, including regulation of cell signaling pathways and survival. In this study, we determined the roles of PEP-1-FK506BP on cell proliferation an...

Journal: :Nephrology 2013
Michelle H T Ta David C H Harris Gopala K Rangan

Interstitial infiltrates, consisting of macrophages and other inflammatory cells, have been consistently reported in human and animal models of polycystic kidney diseases (PKD). However, the mechanisms underlying this inflammation are not well defined. Evidence suggests that interstitial inflammation in PKD is driven by pro-inflammatory chemoattractants such as monocyte chemoattractant protein-...

Journal: :Journal of the American Society of Nephrology : JASN 2002
Bradley K Yoder Xiaoying Hou Lisa M Guay-Woodford

Recent evidence has suggested an association between structural and/or functional defects in the primary apical cilium of vertebrate epithelia and polycystic kidney disease (PKD). In Caenorhabditis elegans, the protein orthologues of the PKD-related proteins, polycystin-1 (LOV-1), polycystin-2 (PKD2), and polaris (OSM-5), co-localize in the cilia of male-specific sensory neurons, and defects in...

2010
Franck Belibi Kameswaran Ravichandran Iram Zafar Zhibin He Charles L. Edelstein

mTORC1/2 and rapamycin in female Han:SPRD rats with polycystic 1 kidney disease (PKD). 2 3 Franck Belibi*, Kameswaran Ravichandran*, Iram Zafar*, Zhibin He and Charles L. 4 Edelstein. 5 6 Division of Renal Diseases and Hypertension, Univ. of Colorado at Denver and the 7 Health Sciences Center, Aurora, Colorado, USA 8 9 *Authors contributed equally to the study 10 11 12 Correspondence to Charles...

Journal: :Development 2004
Zhaoxia Sun Adam Amsterdam Gregory J Pazour Douglas G Cole Mark S Miller Nancy Hopkins

Polycystic kidney disease (PKD) is a common human genetic illness. It is characterized by the formation of multiple kidney cysts that are thought to result from over-proliferation of epithelial cells. Zebrafish larvae can also develop kidney cysts. In an insertional mutagenesis screen in zebrafish, we identified 12 genes that can cause cysts in the glomerular-tubular region when mutated and we ...

2016
Tamio Yamaguchi Jessay G Devassy Md Monirujjaman Melissa Gabbs Harold M Aukema

Rationale for dietary advice in polycystic kidney disease (PKD) is based in part on animal studies that have examined non-orthologous models with progressive development of cystic disease. Since no model completely mimics human PKD, the purpose of the current studies was to examine the effects of dietary soy protein (compared to casein) or oils enriched in omega-3 fatty acids (fish or flax oil ...

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