نتایج جستجو برای: palatecytogeneticspcrpierre robin syndrome sox9

تعداد نتایج: 630150  

2015
Christoph Burdelski Erzen Bujupi Maria Christina Tsourlakis Claudia Hube-Magg Martina Kluth Nathaniel Melling Patrick Lebok Sarah Minner Christina Koop Markus Graefen Hans Heinzer Corinna Wittmer Guido Sauter Waldemar Wilczak Ronald Simon Thorsten Schlomm Stefan Steurer Till Krech Zoran Culig

The transcription factor SOX9 plays a crucial role in normal prostate development and has been suggested to drive prostate carcinogenesis in concert with PTEN inactivation. To evaluate the clinical impact of SOX9 and its relationship with key genomic alterations in prostate cancer, SOX9 expression was analyzed by immunohistochemistry on a tissue microarray containing 11,152 prostate cancers. Da...

Journal: :Development 2009
Brigitte Moniot Faustine Declosmenil Francisco Barrionuevo Gerd Scherer Kosuke Aritake Safia Malki Laetitia Marzi Anne Cohen-Solal Ina Georg Jürgen Klattig Christoph Englert Yuna Kim Blanche Capel Naomi Eguchi Yoshihiro Urade Brigitte Boizet-Bonhoure Francis Poulat

Activation by the Y-encoded testis determining factor SRY and maintenance of expression of the Sox9 gene encoding the central transcription factor of Sertoli cell differentiation are key events in the mammalian sexual differentiation program. In the mouse XY gonad, SOX9 upregulates Fgf9, which initiates a Sox9/Fgf9 feedforward loop, and Sox9 expression is stimulated by the prostaglandin D2 (PGD...

2017
Massilva Rahmoun Rowena Lavery Sabine Laurent-Chaballier Nicolas Bellora Gayle K. Philip Moïra Rossitto Aleisha Symon Eric Pailhoux Florence Cammas Jessica Chung Stefan Bagheri-Fam Mark Murphy Vivian Bardwell David Zarkower Brigitte Boizet-Bonhoure Philippe Clair Vincent R. Harley Francis Poulat

In mammalian embryonic gonads, SOX9 is required for the determination of Sertoli cells that orchestrate testis morphogenesis. To identify genetic networks directly regulated by SOX9, we combined analysis of SOX9-bound chromatin regions from murine and bovine foetal testes with sequencing of RNA samples from mouse testes lacking Sox9. We found that SOX9 controls a conserved genetic programme tha...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2002
Stephan Gasca Joaquin Canizares Pascal De Santa Barbara Catherine Mejean Francis Poulat Philippe Berta Brigitte Boizet-Bonhoure

In mammals, male sex determination starts when the Y chromosome Sry gene is expressed within the undetermined male gonad. One of the earliest effect of Sry expression is to induce up-regulation of Sox9 gene expression in the developing gonad. SOX9, like SRY, contains a high mobility group domain and is sufficient to induce testis differentiation in transgenic XX mice. Before sexual differentiat...

Journal: :Journal of cell science 2015
Wentao Deng Daniel B Vanderbilt Chen-Chung Lin Karen H Martin Kathleen M Brundage J Michael Ruppert

The high mobility group box protein SOX9 and the GLI1 transcription factor play protumorigenic roles in pancreatic ductal adenocarcinoma (PDA). In Kras transgenic mice, each of these factors are crucial for the development of PDA precursor lesions. SOX9 transcription is directly regulated by GLI1, but how SOX9 functions downstream of GLI1 is unclear. We observed positive feedback, such that SOX...

2010
Françoise Coustry Chun-do Oh Takako Hattori Sankar N. Maity Benoit de Crombrugghe Hideyo Yasuda

Mutations in SOX9, a gene essential for chondrocyte differentiation cause the human disease campomelic dysplasia (CD). To understand how SOX9 activates transcription, we characterized the DNA binding and cell-free transcription ability of wild-type SOX9 and a dimerization domain SOX9 mutant. Whereas formation of monomeric mutant SOX9-DNA complex increased linearly with increasing SOX9 concentra...

2011
Claire L. Dubois Hung Ping Shih Philip A. Seymour Nisha A. Patel James M. Behrmann Victoria Ngo Maike Sander

The HMG box transcription factor Sox9 plays a critical role in progenitor cell expansion during pancreas organogenesis and is required for proper endocrine cell development in the embryo. Based on in vitro studies it has been suggested that Sox9 controls expression of a network of important developmental regulators, including Tcf2/MODY5, Hnf6, and Foxa2, in pancreatic progenitor cells. Here, we...

2011
Kevin C. Knower Sabine Kelly Louisa M. Ludbrook Stefan Bagheri-Fam Helena Sim Pascal Bernard Ryohei Sekido Robin Lovell-Badge Vincent R. Harley

BACKGROUND In human embryogenesis, loss of SRY (sex determining region on Y), SOX9 (SRY-related HMG box 9) or SF1 (steroidogenic factor 1) function causes disorders of sex development (DSD). A defining event of vertebrate sex determination is male-specific upregulation and maintenance of SOX9 expression in gonadal pre-Sertoli cells, which is preceded by transient SRY expression in mammals. In m...

2014
Kathleen M. Capaccione Xuehui Hong Katherine M. Morgan Wenyu Liu Michael J. Bishop LianXin Liu Elke Markert Malik Deen Christine Minerowicz Joseph R. Bertino Thaddeus Allen Sharon R. Pine

Sox9 has gained increasing importance both functionally and as a prognostic factor in cancer. We demonstrate a functional role for Sox9 in inducing a mesenchymal phenotype in lung ADC. We show that Sox9 mRNA and protein are overexpressed in lung ADC, particularly those with KRAS mutations. Sox9 expression correlated with the Notch target gene Hes1, and numerous other Notch pathway components. W...

Journal: :American journal of physiology. Gastrointestinal and liver physiology 2012
Laurianne Van Landeghem M Agostina Santoro Adrienne E Krebs Amanda T Mah Jeffrey J Dehmer Adam D Gracz Brooks P Scull Kirk McNaughton Scott T Magness P Kay Lund

Recent identification of intestinal epithelial stem cell (ISC) markers and development of ISC reporter mice permit visualization and isolation of regenerating ISCs after radiation to define their functional and molecular phenotypes. Previous studies in uninjured intestine of Sox9-EGFP reporter mice demonstrate that ISCs express low levels of Sox9-EGFP (Sox9-EGFP Low), whereas enteroendocrine ce...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید