نتایج جستجو برای: linked recessive

تعداد نتایج: 255427  

Journal: :International Journal of Contemporary Pediatrics 2021

Turner syndrome is a commonly encountered chromosomal disorder affecting females, while Duchenne muscular dystrophy severe X-linked recessive males. Although theoretically possible, very few cases of DMD associated with have been reported. We report an 8 year old girl who presented rare association mosaicism (45X/46XringX) dystrophy.

Journal: :American journal of human genetics 2009
Karlien L M Coene Ronald Roepman Dan Doherty Bushra Afroze Hester Y Kroes Stef J F Letteboer Lock H Ngu Bartlomiej Budny Erwin van Wijk Nicholas T Gorden Malika Azhimi Christel Thauvin-Robinet Joris A Veltman Mireille Boink Tjitske Kleefstra Frans P M Cremers Hans van Bokhoven Arjan P M de Brouwer

We ascertained a multi-generation Malaysian family with Joubert syndrome (JS). The presence of asymptomatic obligate carrier females suggested an X-linked recessive inheritance pattern. Affected males presented with mental retardation accompanied by postaxial polydactyly and retinitis pigmentosa. Brain MRIs showed the presence of a "molar tooth sign," which classifies this syndrome as classic J...

Journal: :iranian rehabilitation journal 0
reihaneh alikhani genetic research center, university of social welfare and rehabilitation sciences, tehran, iran. fatemeh ostaresh genetic research center, university of social welfare and rehabilitation sciences, tehran, iran. mojgan babanejad genetic research center, university of social welfare and rehabilitation sciences, tehran, iran. nilofar bazazzadegan genetic research center, university of social welfare and rehabilitation sciences, tehran, iran. hossein najmabadi genetic research center, university of social welfare and rehabilitation sciences, tehran, iran. kimia kahrizi genetic research center, university of social welfare and rehabilitation sciences, tehran, iran.

objectives: hearing loss (hl) is the most common sensory disorder, and affects 1 in 1000 newborns. about 50% of hl is due to genetics and 70% of them are non-syndromic with a recessive pattern of inheritance. up to now, more than 50 genes have been detected which are responsible for autosomal recessive non-syndromic hearing loss, (arnshl). in  iran, hl is one of the most common disabilities due...

Journal: :Clinical journal of the American Society of Nephrology : CJASN 2016
Judy Savige Deb Colville Michelle Rheault Susie Gear Rachel Lennon Sharon Lagas Moira Finlay Frances Flinter

Alport syndrome is an inherited disease characterized by progressive renal failure, hearing loss, and ocular abnormalities. Inheritance is X-linked (85%) or autosomal recessive (15%). Many renal physicians think of Alport syndrome as primarily affecting men. However, twice as many women are affected by the X-linked diseases. Affected women are commonly undiagnosed, but 15%-30% develop renal fai...

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