نتایج جستجو برای: incomplete penetrance

تعداد نتایج: 61081  

Journal: :Cell 2010
Robert J. Johnston Claude Desplan

In recent work published in Nature, Raj et al. (2010) use single mRNA molecule quantification to show that variation in gene expression in Caenorhabditis elegans increases in mutants displaying incomplete penetrance. They find that a bimodal response is triggered when noisy expression of an upstream regulator crosses a critical threshold.

2017
Maria Franaszczyk Przemyslaw Chmielewski Grazyna Truszkowska Piotr Stawinski Ewa Michalak Malgorzata Rydzanicz Malgorzata Sobieszczanska-Malek Agnieszka Pollak Justyna Szczygieł Joanna Kosinska Adam Parulski Tomasz Stoklosa Agnieszka Tarnowska Marcin M Machnicki Bogna Foss-Nieradko Malgorzata Szperl Agnieszka Sioma Mariusz Kusmierczyk Jacek Grzybowski Tomasz Zielinski Rafal Ploski Zofia T Bilinska

TTN gene truncating variants are common in dilated cardiomyopathy (DCM), although data on their clinical significance is still limited. We sought to examine the frequency of truncating variants in TTN in patients with DCM, including familial DCM (FDCM), and to look for genotype-phenotype correlations. Clinical cardiovascular data, family histories and blood samples were collected from 72 DCM pr...

Journal: :Brain & Development 2021

Abstract Background The periodic paralyses are a group of skeletal muscle channelopathies caused by variants in several ion channel genes. Potassium Inwardly Rectifying Channel Subfamily J Member 5 (KCNJ5) encodes the G-protein–activated inwardly rectifying potassium 4 (Kir3.4) and heterozygous KCNJ5 cause familial hyperaldosteronism long QT syndrome (LQTS). Recent studies suggested that also c...

Journal: :Cancer epidemiology, biomarkers & prevention : a publication of the American Association for Cancer Research, cosponsored by the American Society of Preventive Oncology 2005
Valérie Chaudru Karine Laud Marie-Françoise Avril Annie Minière Agnès Chompret Brigitte Bressac-de Paillerets Florence Demenais

Germline mutations in CDKN2A gene predispose to melanoma with high but incomplete penetrance. Penetrance of CDKN2A gene was found to be significantly influenced by host factors (nevus phenotypes and sunburn) on one hand and by variants of MC1R gene (RHC variants consistently associated with red hair and fair skin) on the other hand. Our goal was to examine the joint effects of MC1R variants and...

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