Purpose. Extraskeletal osteosarcoma represents an unusual soft-tissue sarcoma that historically is reported to carry an exceptionally poor prognosis.The objectives of this study were to use a prospectively gathered sarcoma database to test the prevailing clinical bias and more accurately describe the natural history, characterize the prognostic features, estimate survival and evaluate treatment...

BACKGROUND Extraskeletal Ewings sarcoma are rare tumors for which there is no consensus on optimal management. METHODS A retrospective review of the clinical features, treatment and outcome of patients with extraskeletal Ewings sarcoma who reported to a single institution between January 1992-December 2003 is reported. RESULTS A total of 19 patients with extraskeletal Ewings sarcoma were id...

Extraskeletal chondroma is a benign cartilaginous tumor that occurs predominantly in the soft tissues near small joints of the hands and feet. There are rare reports of the lesion in other sites, such as the head, neck, trunk, oral cavity, larynx, and pharynx. We present a case of an axillary mass in a 15-year-old girl who underwent MRI examination and resection, with the ultimate diagnosis of ...

Chondrosarcoma is an uncommon malignant neoplasm of cartilaginous origin. Extraskeletal chondrosarcomas are far less common than their intraosseous counterparts, representing approximately 2% of all soft tissue sarcomas. Clinically, extraskeletal mesenchymal chondrosarcoma (EMC) shows a very fast progression. It also has a high incidence of local recurrence and distant metastasis. The most comm...

Sinonasal and pharyngeal mass lesion of Extraskeletal Ewing sarcomas (EEWSs) are extremely rare. Herein we present a case EEWSs ethmoid sinus extending into nasal spaces mimicking as angiofibroma clinically. Histopathological examination in conjunction with immunohistochemistry puzzled out the diagnostic dilemma.

OBJECTIVES To report characteristics, treatment, and outcomes for an international cohort of patients with extraskeletal osteosarcoma (ESOS). MATERIALS AND METHODS Through the Rare Cancer Network, retrospective data on patients with ESOS were collected. Patient characteristics, multimodality treatment information, and survival status were analyzed. RESULTS Thirty-seven patients in 4 health ...

The extraskeletal myxoid chondrosarcoma (CME) is a rare malignant soft tissue tumour described as a distinct clinical, histological, immunohistochemical, genetical and evolutive entity. It represents only 2.5% of soft tissue sarcomas. Its individualization is important because it has a long and indolent clinical course, and tumour-related death often occurs after a long survival period. The dia...

Patient. We report a 22-year-old male presenting with extraskeletal osteosarcoma of the orbit.Discussion. Extra skeletal osteosarcomas are uncommon tumours, usually arising from the lower extremities or girdle. These are aggressive tumours with high metastatic potential and poor outcome. Optimal treatment is undefined, and the role of radical surgery, radiotherapy and aggressive chemotherapy is...

Extraskeletal myxoid chondrosarcomas usually arise deep in the proximal extremities and limb girdles. Patients with this type of sarcoma have high rates of local recurrence and metastases, but do not typically have paraneoplastic syndromes. We report an unusual case of a 49-year-old man with anti-Hu syndrome in the setting of an extraskeletal myxoid chondrosarcoma. This case shows the importanc...