This report describes the anesthetic management of a patient with Ehlers-Danlos syndrome type IV. This is one of the rare genetic disorder which can present both in emergency and as a scheduled surgical case.

Fatal spontaneous rupture of the lower abdominal aorta in a previously healthy 61-year-old woman is reported; the possibility that she had the Ehlers-Danlos syndrome is discussed.

A case of Ehlers Danlos syndrome is described in a 54-year-old Caucasian male. He had calcific aortic valve disease and dilatation of the ascending aorta. An aortic valve replacement was performed using a Starr prosthesis.

The Ehlers-Danlos syndrome is a group of inherited connective tissue disorders caused by defects in collagens or tenascin-X (TNX). Muscle involvement can be expected based on interactions between muscle and extracellular matrix molecules; however, muscle function has not yet been investigated quantitatively. This study aims to investigate effects of TNX deficiency on muscular characteristics in...

A 2-year-old girl was referred to our clinic for evaluation of Ehlers-Danlos syndrome. She had a history of easy bruising, and the physical examination showed hematomas, stretchy skin of velvety texture, and hyperflexible joints, suggestive of the presumed diagnosis. Her father had fullblown Ehlers-Danlos syndrome of the classic type featuring skin hyperextensibility, widened atrophic scars, an...

Celiprolol is a β-blocker with a unique pharmacologic profile: it is a β1-andrenoceptor antagonist with partial β2 agonist activity. Given this combination of effects, celiprolol may be better described as a selective adrenoreceptor modulator. It has antihypertensive and antianginal properties and is indicated for those uses in various countries around the world. In the United States, however, ...

UNLABELLED A 51-year-old man with Ehlers-Danlos syndrome presented to our emergency department with the chief complaint of chest tightness. The patient was diagnosed with acute coronary syndrome, due to his crescendo pattern of typical angina without elevated troponin-I, which was managed with dual-antiplatelet agents and intravenous heparinization. However, the symptoms persisted, and coronary...

conclusions all clinical findings were directly related to the features described for eds. there are occasions when dentists would be the first health professionals to see these individuals at a young age; knowing the classic signs of eds could help in identifying and managing them properly. introduction this study aimed to elaborate a case with several complications and recommended some sugges...