The granulomatosis with polyangiitis, initially known as Wegener's granulomatosis, is a small and medium vessels vasculitis. It's classic form presents a triad: necrotizing granuloma of respiratory tract, necrotizing cutaneous vasculitis and glomerulonephritis. This vasculitis has cytoplasmic antineutrophil antibodies as signal. This work illustrates a case, of multisystemic rare disease, in wh...

We describe a 36-year-old woman with livedo vasculitis (atrophie blanche) lasting for 15 years. After the failure of numerous therapeutic modalities the patient was treated with intravenous immunoglobulin. Significant resolution of the cutaneous lesions was seen with a concomitant alleviation of pain. To the best of our knowledge this is the first patient with livedo vasculitis described in the...

Two cases of systemic antineutrophil cytoplasmic antibody (ANCA) vasculitis in the setting of chronic lymphocytic leukaemia and angioimmunoblastic lymphadenopathy type T cell lymphoma are reported. The two patients had fever of unknown origin associated with cutaneous vasculitis and "pulmonary-renal syndrome" with alveolar haemorrhage. Despite anti-infectious treatments, steroids, and chemother...

BACKGROUND Omega-3 fatty acids (O3FA) have been used to treat IgA nephropathy (IgAN) but not cutaneous IgA vasculitis (IgAV). CASE REPORT A 47-year-old female was referred for cutaneous vasculitis. She had a 24-year history of flares of palpable purpura, arthralgia associated with hematuria, and proteinuria. We diagnosed cutaneous IgAV associated with IgAN. We administered prednisone at doses...

An 8-year-old, spayed, female shar-pei with an earlier clinical diagnosis of autoinflammatory disease presented fever and plaque-nodular ulcerative dermatitis. Dermatopathological examination was compatible diffuse, non-septal, neutrophilic panniculitis leukocytoclastic vasculitis, bacterial culture negative. Good response to prednisone treatment seen. Based on this case, cutaneous sterile vasc...

A 60-year-old man presented with cutaneous vasculitis, leucopenia and psoriasis. He was treated initially with ciclosporin A. On withdrawal of ciclosporin, due to inadequate improvement of cutaneous vasculitis, he developed psoriatic arthritis. Worsening neutropenia and pancytopenia, believed to be immune mediated, developed. He was treated with prednisolone, methotrexate and adalimumab but dev...

AIM To characterize the clinicopathologic features and to assess the therapeutic outcome in cutaneous vasculitis. MATERIAL AND METHODS Fifty biopsy proven cases of cutaneous vasculitis seen between January 1998 and July 1999 were studied. RESULTS The commonest presentation was palpable purpura. The site most commonly affected was the extremity, irrespective of the age (adults - 40 and child...

Cutaneous polyarteritis nodosa is an infrequent necrotizing vasculitis of small and medium-sized arteries, with a recurrent and chronic course, that can be associated with fever, arthralgia, myalgia and neuropathy without visceral involvement. We report a cutaneous polyarteritis nodosa case.