نتایج جستجو برای: congenital stationary night blindness

تعداد نتایج: 223938  

Journal: :Seizure 2002
Yasuhiro Manabe Hisashi Narai Hitoshi Warita Takeshi Hayashi Yoshihiko Shiro Kenichi Sakai Kenichi Kashihara Mikio Shoji Koji Abe

This is the first report of benign adult familial myoclonic epilepsy (BAFME) with night blindness. Our cases of BAFME (mother, son, and daughter) demonstrated night blindness with a reduced b-wave response on electroretinography (ERG) suggesting an alteration in calcium-mediated neurotransmitter release from photoreceptors in response to light. Several familial epilepsies have been shown to be ...

Journal: :EMBO reports 2016
Ankita Singhal Ying Guo Milos Matkovic Gebhard Schertler Xavier Deupi Elsa Cy Yan Joerg Standfuss

Congenital stationary night blindness (CSNB) is an inherited and non-progressive retinal dysfunction. Here, we present the crystal structure of CSNB-causing T94I2.61 rhodopsin in the active conformation at 2.3 Å resolution. The introduced hydrophobic side chain prolongs the lifetime of the G protein activating metarhodopsin-II state by establishing a direct van der Waals contact with K2967.43, ...

Journal: :Vision Research 2008
Mineo Kondo Shinji Ueno Chang-Hua Piao Yozo Miyake Hiroko Terasaki

Focal macular cone electroretinograms (ERGs) and multifocal ERGs were recorded to study the macular function in patients with the complete-type of congenital stationary night blindness (cCSNB). The waveforms of the focal macular cone ERGs and the on- and off-responses of the multifocal ERGs in the cCSNB patients were similar to those recorded from monkey retinas treated with L-2 amino-4-phospho...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید