نتایج جستجو برای: ceramidase

تعداد نتایج: 515  

2012
Konrad SANDHOFF

Analysis of lipid storage in postmortem brains of patients with amaurotic idiocy led to the recognition of five lysosomal ganglioside storage diseases and identification of their inherited metabolic blocks. Purification of lysosomal acid sphingomyelinase and ceramidase and analysis of their gene structures were the prerequisites for the clarification of Niemann-Pick and Farber disease. For lipi...

Journal: :Frontiers in bioscience : a journal and virtual library 2008
Xiang Liu Saeed Elojeimy Lorianne S Turner Ayman E M Mahdy Youssef H Zeidan Alicja Bielawska Jacek Bielawski Jian-Yun Dong Ahmed M El-Zawahry Gui-wen Guo Yusuf A Hannun David H Holman Semyon Rubinchik Zdzislaw Szulc Thomas E Keane Mahvash Tavassoli James S Norris

During the last decade, sphingolipid deregulation, namely the balance between the pro-apoptotic molecule ceramide and the anti-apoptotic sphingolipid sphingosine-1-phosphate, has emerged as an important factor in cancer pathology and resistance to therapy. Thus, our research has been focused on developing drugs that are able to restore normal sphingolipid balance, precisely through increasing t...

2012
Nobutomo Ikarashi Wataru Sato Takahiro Toda Makoto Ishii Wataru Ochiai Kiyoshi Sugiyama

We examined the inhibitory effect of polyphenol-rich aqueous extract from the bark of Acacia mearnsii (PrA) on itching associated with atopic dermatitis (AD). HR-1 mice were fed a normal diet, special diet (AD group), or special diet containing 3% PrA (PrA group) for 6 weeks. In the AD group, itching frequency and transepidermal water loss increased compared to the control group. In the PrA gro...

Journal: :Haematologica 2015
Shaalee Dworski Alexandra Berger Caren Furlonger Joshua M Moreau Makoto Yoshimitsu Jessa Trentadue Bryan C Y Au Christopher J Paige Jeffrey A Medin

Journal: :Journal of lipid research 2010
Carmen Bedia Luz Camacho José Luís Abad Gemma Fabriàs Thierry Levade

Acid ceramidase (aCDase) is one of several enzymes responsible for ceramide degradation within mammalian cells. As such, aCDase regulates the intracellular levels of the bioactive lipid ceramide. An inherited deficiency of aCDase activity results in Farber disease (FD), also called lipogranulomatosis, which is characterized by ceramide accumulation in the tissues of patients. Diagnosis of FD is...

Journal: :Journal of Biological Chemistry 2001

Journal: :Journal of Lipid Research 2002

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