نتایج جستجو برای: aldrich syndrome

تعداد نتایج: 623385  

Journal: :Blood 2001
A H Filipovich J V Stone S C Tomany M Ireland C Kollman C J Pelz J T Casper M J Cowan J R Edwards A Fasth R P Gale A Junker N R Kamani B J Loechelt D W Pietryga O Ringdén M Vowels J Hegland A V Williams J P Klein K A Sobocinski P A Rowlings M M Horowitz

Human leukocyte antigen (HLA)-identical sibling bone marrow transplantation is an effective treatment for Wiskott-Aldrich syndrome. However, most children with this disease lack such donors and many patients receive transplants from alternative donors. This study compared outcomes of HLA-identical sibling, other related donor, and unrelated donor transplantation for Wiskott-Aldrich syndrome. Th...

Journal: :The Journal of clinical investigation 1971
R M Blaese W Strober A L Levy T A Waldmann

The Wiskott-Aldrich syndrome is an immune deficiency disorder with an impairment of both humoral and cellular immune responses. Metabolic turnover studies of IgG, IgA, IgM, and albumin were conducted in seven patients with the Wiskott-Aldrich syndrome using purified radioiodinated proteins. The survival of each of the proteins studied was significantly shortened with a half-time of 7.5 days for...

Journal: :Nihon Rinsho Men'eki Gakkai kaishi = Japanese journal of clinical immunology 2005
Yoji Sasahara Shigeru Tsuchiya

The Wiskott-Aldrich syndrome (WAS) is an X-linked primary immunodeficiency caused by mutations in the gene encoding the WAS protein (WASP). WASP is predominantly expressed in hematopoietic cells and regulates the reorganization of the actin cytoskeleton in response to various important cell stimuli including T cell receptor signaling. WASP is localized at the immunological synapses between T ce...

2014
Sven H. Petersen Anton Sendel Mirjam van der Burg Lisa S. Westerberg

Human immunology is entering the next frontier. With the fast developing technology, we can today sequence the whole genome from an individual in a relatively short time. It is now possible to decipher pathological mechanisms in immunological diseases, including primary immunodeficiencies, with high specificity. A particularly interesting aspect to study is the development and maintenance of th...

Journal: :The New England journal of medicine 2006
Jennifer M Puck Fabio Candotti

Scandlen G. Consumer-driven health care: just a tweak or a revolution? Health Aff (Millwood) 2005;24:1554-8. Claxton G, Gabel J, Gil I, et al. Health benefits in 2006: premium increases moderate, enrollment in consumer-directed health plans remains modest. Baltimore: Health Affairs, September 26, 2006 (Web Exclusive). Remler DK, Glied SA. How much more cost sharing will health savings accounts 1.

Journal: :Blood 1988
E R Fearon D B Kohn J A Winkelstein B Vogelstein R M Blaese

The Wiskott-Aldrich syndrome (WAS) is an X-linked recessive disease characterized by immunodeficiency and severe thrombocytopenia in affected males, but no demonstrable clinical abnormalities in carrier females. Through analysis of the methylation patterns of X-linked genes that display restriction fragment length polymorphisms (RFLPs), we studied the pattern of X-chromosome inactivation in var...

Journal: :Blood 1996
E Remold-O'Donnell F S Rosen D M Kenney

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