purpose: to report an extremely rare presentation of isolated orbital xanthogranuloma with no systemic disease, nor dermatologic manifestation. case report: the patient was a 45-year-old man complaining of a mass lesion in the superior and inferior eyelids of his right eye; the lesions had been enlarging slowly and painlessly since 5 years before. other examinations (including skin, heart, etc....

Necrobiotic xanthogranuloma is a rare disease characterized by indurated nodules and yellowish-red plaques in the dermis or subdermal tissues particularly in the periorbital region; the lesions are often ulcerated. This disease is frequently associated with hematological disorders such as monoclonal gammopathy and lymphoproliferative disorders. Its pathogenesis is unknown and the small number o...

© 2014 The Authors. doi: 10.2340/00015555-1712 Journal Compilation © 2014 Acta Dermato-Venereologica. ISSN 0001-5555 Juvenile xanthogranuloma (JXG) is a non-Langerhans histiocytosis occurring predominantly in infancy and early childhood. Resolution usually occurs over a period of months to several years, and it is rare for the condition to persist beyond late childhood (1). The symmetrical gian...