نتایج جستجو برای: willi syndrome

تعداد نتایج: 622258  

Journal: :Genetics and molecular research : GMR 2014
C F Rocha C L A Paiva

Prader-Willi syndrome (PWS) is caused by the lack of expression of genes located on paternal chromosome 15q11-q13. This lack of gene expression may be due to a deletion in this chromosomal segment, to maternal uniparental disomy of chromosome 15, or to a defect in the imprinting center on 15q11-q13. PWS is characterized by hypotonia during the neonatal stage and in childhood, accompanied by a d...

Journal: :International journal of spine research 2021

Prader-Willi Syndrome (PWS) is a complex, neurogenetic, multisystem disorder with prevalence of 1:15000 to 1:30000, caused by lack expression genes in the paternally inherited chromosome 15q 11.2-q13. In this report we aim characterize and increase awareness kyphoscoliosis these children.

Journal: :Archives of Disease in Childhood 1994

Journal: :Journal of Armed Forces Medical College, Bangladesh 1970

2016
Alexandre Slowetzky Amaro Maria Cristina Triguero Veloz Teixeira Maria Luiza Guedes de Mesquita Graciele Massoli Rodrigues Daniela Andrea Rubin Luiz Renato Rodrigues Carreiro

BACKGROUND Physical activity programs are a powerful tool against several diseases including obesity and their comorbidities. Prader-Willi syndrome is the most common genetic disease associated with obesity, and brings with it behavioral and emotional problems that need complex management. Research into the effect of physical activity programs on Prader-Willi syndrome is limited and it is frequ...

Journal: :The Journal of neuroscience : the official journal of the Society for Neuroscience 2008
Sébastien Zanella Françoise Watrin Saïda Mebarek Fabienne Marly Michel Roussel Catherine Gire Gwenaëlle Diene Maïté Tauber Françoise Muscatelli Gérard Hilaire

Prader-Willi syndrome is a neurogenetic disease resulting from the absence of paternal expression of several imprinted genes, including NECDIN. Prader-Willi children and adults have severe breathing defects with irregular rhythm, frequent sleep apneas, and blunted respiratory regulations. For the first time, we show that Prader-Willi infants have sleep apneas already present at birth. In parall...

Journal: :Patient education and counseling 1999
H W van den Borne R H van Hooren M van Gestel P Rienmeijer J P Fryns L M Curfs

The aim of the present study was to identify the psychosocial problems of parents of a child with Prader-Willi syndrome or a child with Angelman syndrome. In addition, the strategies these parents apply to cope with these problems as well as their need for information are described. To assess these topics, parents filled in a self-report questionnaire. Both parent groups were found to have a hi...

Journal: :Archives of disease in childhood 1969
B T Rudd G W Chance C G Theodoridis

In 1956 Prader, Labhart, and Willi first described a group of patients who presented with 'floppiness' at birth and later became obese, dwarfed, and mentally retarded, and some had impaired glucose tolerance tests. Further articles followed (Prader and Willi, 1961; Laurance, 1961, 1967; Forssman and Hagberg, 1964; Evans, 1964; Hooft, Delire, and Casneuf, 1966). Laurance gave a detailed descript...

Journal: :The Journal of clinical investigation 2013
Amélie Bonnefond Anne Raimondo Fanny Stutzmann Maya Ghoussaini Shwetha Ramachandrappa David C Bersten Emmanuelle Durand Vincent Vatin Beverley Balkau Olivier Lantieri Violeta Raverdy François Pattou Wim Van Hul Luc Van Gaal Daniel J Peet Jacques Weill Jennifer L Miller Fritz Horber Anthony P Goldstone Daniel J Driscoll John B Bruning David Meyre Murray L Whitelaw Philippe Froguel

Sim1 haploinsufficiency in mice induces hyperphagic obesity and developmental abnormalities of the brain. In humans, abnormalities in chromosome 6q16, a region that includes SIM1, were reported in obese children with a Prader-Willi-like syndrome; however, SIM1 involvement in obesity has never been conclusively demonstrated. Here, SIM1 was sequenced in 44 children with Prader-Willi-like syndrome...

1998
Andrés Martin Elizabeth M. Dykens Suzanne B. Cassidy James F. Leckman

Prader-Willi syndrome is a genetic disorder characterized by mental retardation, dysmorphic features, and behavioral dysfunction, most notably food-related problems such as hyperphagia, food seeking, and a high risk for obesity (1). Although food-related symptoms are a hallmark of the disorder, other psychiatric manifestations are common and can lead to significant interference in the affected ...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید