Eight cases are reported in which complete transposition of the great vessels was associated with varying degrees of hypoplasia of the right ventricle. In three, the correct diagnosis was suspected on the basis of certain electrovectorcardiographic findings and confirmed by selective angiography. Quantitative analysis of ventricular volumes and valve circumferences demonstrated that these cases...

CONGENITAL stenotic lesions of the mitral valve may be classified into various groups depending on the functional capacity of the left ventricle. In the extreme form, s8vere stenosis or atresia of the mitral valve is associated with hypoplasia of the left ventricle and aorta. Septal defects are usually present and these combinations are lethal in infaincy.i' 2 In the presence of a functioning l...

In the present case report, we describe a malformation consisting of a double-outlet right ventricle with an intact ventricular septum diagnosed in a 3-day-old female newborn. To our knowledge 35 cases have been described in the literature. The diagnosis was made by two-dimensional echocardiography and confirmed by angiocardiography. An inadequate opening in the interatrial septum and hypoplasi...

[1] Morell VO, Wearden PD. Aortic translocation for the management of transposition of the great arteries with a ventricular septal defect, pulmonary stenosis, and hypoplasia of the right ventricle. Eur J Cardiothorac Surg 2007;31:552—4. [2] Sayin OA, Ugurlucan M, Saltik L, Sungur Z, Tireli E. Modified Nikaidoh procedure for transposition of great arteries, ventricular septal defect and left ve...

An ectopic posterior pituitary gland is a rare condition and may present with an empty pituitary fossa, hypoplasia or absence of the infundibular stalk and resultant short stature due to growth hormone deficiency. The location of the ectopic lobe can vary, but it is most commonly situated along the median eminence in the floor of the third ventricle. We report a case of an ectopic posterior pit...

Dandy-Walker malformation is characterised by agenesis or hypoplasia of the cerebellar vermis, cystic dilatation of the fourth ventricle, and enlargement of the posterior fossa. Approximately 70-90% of patients have hydrocephalus. Lissencephaly is characterised by absence (agyria) or incomplete development (pachygyria) of the gyri of the cerebral cortex, causing the brain's surface to appear un...

Hypoplasia of the right ventricle is uncommon as an isolated entity. It may result from tricuspid atresia, but is most commonly secondary to pulmonary atresia with intact ventricular septum. Pulmonary atresia with intact ventricular septum is rare, accounting for 1-3% of cases of congenital heart disease. It occurs in 0.1 to 0.4 in 10,000 live births. Pulmonary atresia with intact ventricular s...

This is a case report of an 8-month-old infant with congenital heart disease including; pulmonary atresia, intact ventricular septum, right ventricular hypoplasia, atrial septal defect, coronary sinusoids (fistulas between right ventricle and left anterior descending artery). The patient had a stent for patent ductus arteriosus at 3 months of age and after 4 months a bidirectional Glenn shunt o...

The morphology of the common atrioventricular valve and its relation to the ventricles was assessed by cross sectional echocardiography in 17 patients with atrial isomerism--four with left isomerism and 13 with right isomerism. In 13 patients the atrioventricular valve consisted of four leaflets: a large anterosuperior leaflet, two lateral leaflets, and a posteroinferior leaflet. The remaining ...

Left ventricular isolated hypoplasia is a seldom-described cardiac abnormality. Right usually associated with congenital anomalies of the pulmonary or tricuspid valve, whereas biventricular apical has never been described. We report case 48-year-old man no history known disease who was found to have complex abnormality characterized by: 1) Deficiency myocardium within apex adipose tissue infilt...