Susac syndrome (SS) or retino-cochleo-cerebral vasculopathy is an extremely rare, severe, and potentially disabling condition. Underlying occlusive microangiopathy in SS clinically characterized by the triad of encephalopathy, sensorineural hearing loss branch retinal arterial occlusion. therapy envisages simultaneous use high doses glucocorticoids, intravenous immunoglobulins, cyclophosphamide...

A 29 year old male was admitted at the emergency room suffering from gradually worsening headache followed by nausea. In the hospital patient presented with lethargy, reduction of consciousness level and bilateral hypoacusis. Ophthalmic examination and fluorescein angiography showed retinal vasculitis. This finding was crucial to the diagnosis of Susac syndrome, a rare disease characterized by ...

We describe the case of a twenty-year-old woman with subacute encephalopathy, who subsequently developed hearing loss and ophtalmopathy. The clinical triad and typical findings on magnetic resonance imaging and cerebrospinal fluid analysis led to the diagnosis of Susac syndrome. Brain positron emission tomography showed abnormalities which are comparable with other types of central nervous syst...

Retino-cochleo-cerebral angiopathy or Susac syndrome is a rare autoimmune disease that selectively affects the vessels of retina, inner ear and central nervous system. Differentiation multiple sclerosis presents difficulties due to similarity MRI semiotics these two diseases. This article clinical cases patients with who were diagnosed at onset disease. Based on analysis our own observations li...