Fibrodysplasia ossificans progressiva (FOP) is a severely disabling heritable disorder of connective tissue characterized by congenital malformations of the great toes and progressive heterotopic ossification that forms qualitatively normal bone in characteristic extraskeletal sites. The worldwide prevalence is approximately 1/2,000,000. There is no ethnic, racial, gender, or geographic predile...

The risk of osseous bridge development after certain types of physeal injury is well established. Once formed, the bridge continues to grow and results in a progressive deformity. The authors present an unusual case of a five-year-old girl who had a Salter-Harris Type-IV fracture of the distal tibial epiphyseal plate, with subsequent osseous bridge formation and deformity development. The bridg...

Fibrous dysplasia is a benign bone disease first described by Lichtenstein in 1938. It is characterized by progressive replacement of normal bone with fibro-osseous connective tissue. When the disease involves craniofacial skeleton, it results in significant disfigurement and other functional problems. This paper reports a case of large craniofacial fibrous dysplasia involving zygomaticomaxilla...

Vertebral hemangiomas are common lesions and usually considered benign. A rare subset of them, however, are characterized by extra-osseous extension, bone expansion, disturbance of blood flow, and occasionally compression fractures and thereby referred to as aggressive hemangiomas. We present a case of a 67-year-old woman with progressive paraplegia and an infiltrative mass of T4 vertebra causi...

introduction camurati-engelmann disease (ced) is a rare autosomal dominant disease with various phenotypic expressions. the symptoms usually develop during childhood. the hallmark of the disease is bilateral symmetric diaphyseal hyperostosis of the long bones with progressive involvement of the metaphysis. the epiphysis is strictly spared. the common clinical symptoms are pain of the extremitie...

Fibrous dysplasia (FD) is a slowly progressive, benign, chronic fibro-osseous tissue disease, which is characterized by abnormal proliferation of fibrous tissue interspersed with normal or immature bone. In this report we describe a patient with monostotic fibrous dysplasia that involved temporal bone presenting with vertigo, and discuss diagnostic work-up, histopathology, and treatment options...

Parry Romberg syndrome (PRS), also referred to as progressive hemifacial atrophy, facial hemiatrophy, or idiopathic was first described by C and M Romberg.1 It manifests in the two decades morphologically normal-born individuals. commonly affects one more dermatomes trigeminal nerve territory. has an early onset of ophthalmic neurological involvement a variable maxillo-facial cardiac involvemen...

Osteonecrosis of the femoral head is a progressive disease. Without operative intervention, it most often results in collapse and deterioration of the joint. Many joint-preserving surgeries have been implemented, but no uniform treatment exists. The authors report a modified technique of tantalum rod implantation combined with vascularized iliac grafting for the treatment of osteonecrosis of th...

Hodgkin's lymphoma (HL) is one of the few adult malignancies that most frequently presents with a progressive, painless enlargement of the peripheral lymph nodes. A primary osseous presentation of HL, without lymph node involvement, is extremely rare. The present study describes a case of primary multifocal osseous HL in a 22-year-old female. The patient presented with pain in the lumbar-sacral...