نتایج جستجو برای: macrophage activating syndrome hemophagocytic lymphohistiosytosis

تعداد نتایج: 728386  

Journal: :Anticancer research 2015
Toshio Inui Kentaro Kubo Daisuke Kuchiike Yoshihiro Uto Takahito Nishikata Norihiro Sakamoto Martin Mette

BACKGROUND Gc protein-derived macrophage-activating factor (GcMAF) immunotherapy has been steadily advancing over the last two decades. Oral colostrum macrophage-activating factor (MAF) produced from bovine colostrum has shown high macrophage phagocytic activity. GcMAF-based immunotherapy has a wide application for use in treating many diseases via macrophage activation or for use as supportive...

Journal: :Haematologica 2015
Sebastian Fn Bode Sandra Ammann Waleed Al-Herz Mihaela Bataneant Christopher C Dvorak Stephan Gehring Andrew Gennery Kimberly C Gilmour Luis I Gonzalez-Granado Ute Groß-Wieltsch Marianne Ifversen Jenny Lingman-Framme Susanne Matthes-Martin Rolf Mesters Isabelle Meyts Joris M van Montfrans Jana Pachlopnik Schmid Sung-Yun Pai Pere Soler-Palacin Uta Schuermann Volker Schuster Markus G Seidel Carsten Speckmann Polina Stepensky Karl-Walter Sykora Bianca Tesi Thomas Vraetz Catherine Waruiru Yenan T Bryceson Despina Moshous Kai Lehmberg Michael B Jordan Stephan Ehl

Hemophagocytic lymphohistiocytosis is a hyperinflammatory syndrome defined by clinical and laboratory criteria. Current criteria were created to identify patients with familial hemophagocytic lmyphohistiocytosis in immediate need of immunosuppressive therapy. However, these criteria also identify patients with infection-associated hemophagocytic inflammatory states lacking genetic defects typic...

Journal: :Jornal brasileiro de pneumologia : publicacao oficial da Sociedade Brasileira de Pneumologia e Tisilogia 2012
Thiago Prudente Bártholo José Gustavo Pugliese Thiago Thomaz Mafort Vinicius Lemos da Silva Cláudia Henrique da Costa Rogério Rufino

Although hemophagocytic syndrome is a rare clinical condition, it is associated with high mortality and the number of cases described in the literature has progressively increased. The diagnosis of hemophagocytic syndrome is made on the basis of a finding of hemophagocytosis. Sarcoidosis is a highly prevalent disease whose course and prognosis might correlate with the initial clinical presentat...

2017
Abdul Rashid Shah Tariq Muzzafar Rita Assi Dawid Schellingerhout Zeev Estrov Gevorg Tamamyan Hagop Kantarjian Naval Daver

Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of severe immune activation with macrophage and T-cell infiltration resulting in, multi organ damage. HLH may be primary or secondary in etiology. A high index of suspicion is essential for early diagnosis and treatment. Diagnostic criteria need to be refined and newer treatment options to be explored in order to improve survival especially...

2015
Guido Granata Dario Didona Giuseppina Stifano Aldo Feola Massimo Granata

Macrophage activation syndrome (MAS) is a potentially fatal condition. It belongs to the hemophagocytic lymphohistiocytosis group of diseases. In adults, MAS is rarely associated with systemic lupus erythematosus, but it also arises as complication of several systemic autoimmune disorders, like ankylosing spondylitis, rheumatoid arthritis, and adult-onset Still's disease. Several treatment opti...

2016
Jed A. Katzel

Hemophagocytic Lymphohistiocytosis (HLH) is a rare, lifethreatening syndrome of excessive multisystem inflammation and tissue destruction due to abnormal immune activation. It is more frequently seen in the pediatric population, either as a genetic disorder or secondary to infection or autoimmune disease, but can present in acquired forms at any age. It is thought to be due to an absence of dow...

2011
Jan-Inge Henter AnnaCarin Horne Bo Magnusson Stefan Hagelberg

Background/aim Rheuma-associated hemophagocytic lymphohistiocytosis (Rh-HLH), also called macrophage activation syndrome (MAS), is a severe complication of systemic inflammatory disorders. Rh-HLH has clinical and laboratory similarities to other forms of HLH, and is potentially life threatening. Treatment of Rh-HLH has not been standardized yet, but it commonly includes a variety of agents such...

2016
E. Scott Halstead Surender Rajasekaran Julie C. Fitzgerald Scott L. Weiss

We describe a case of an infant with HSV meningitis and septic shock who demonstrated a remarkably high serum ferritin level. Aggressive pediatric intensive care and the administration of high-dose glucocorticoids were not able to reverse the multiple organ dysfunctions. Subsequent autopsy identified the presence of hemophagocytosis, thus the patient fulfilled hemophagocytic lymphohistiocytosis...

2015
G Prencipe I Caiello C Bracaglia C de Min F De Benedetti

Introduction Macrophage activation syndrome is a term used to identify hemophagocytic lymphohistiocytosis secondary to rheumatic diseases (rheuHLH). It is a severe, potentially fatal condition that occurs in the context of rheumatic diseases, particularly systemic juvenile idiopathic arthritis. It is part of secondary HLH forms, that are clinically and biochemically similar to primary HLH (pHLH...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید