نتایج جستجو برای: lysosomal disorders

تعداد نتایج: 684439  

Journal: :Philosophical transactions of the Royal Society of London. Series B, Biological sciences 2003
Volkmar Gieselmann Ulrich Matzner Diana Klein Jan Eric Mansson Rudi D'Hooge Peter D DeDeyn Renate Lüllmann Rauch Dieter Hartmann Klaus Harzer

Lysosomal storage diseases comprise a group of about 40 disorders, which in most cases are due to the deficiency of a lysosomal enzyme. Since lysosomal enzymes are involved in the degradation of various compounds, the diseases can be further subdivided according to which pathway is affected. Thus, enzyme deficiencies in the degradation pathway of glycosaminoglycans cause mucopolysaccharidosis, ...

Journal: :Food frontiers 2023

Autophagy-lysosomal pathway (ALP), a lysosome-mediated self-renewal process, is crucial for cell survival and death. Acrylamide (AA) neurotoxic compound produced during food thermal processing, the mechanism underlying AA-induced neurotoxicity remains elusive. In this study, we explored whether dysregulated ALP was involved in mechanism. We first evaluated toxic effects of AA on activation apop...

Journal: :Trends in neurosciences 2011
Mark L Schultz Luis Tecedor Michael Chang Beverly L Davidson

Lysosomal storage diseases (LSDs) are a class of metabolic disorders caused by mutations in proteins critical for lysosomal function. Such proteins include lysosomal enzymes, lysosomal integral membrane proteins, and proteins involved in the post-translational modification and trafficking of lysosomal proteins. There are many recognized forms of LSDs and, although individually rare, their combi...

Journal: :Biochimica et Biophysica Acta (BBA) - Molecular Cell Research 2009

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید