congenital cutis laxa is an exceptional condition. no large scale pedigree has been reported from iran. we report a family with 106 members with two members affected with cutis laxa. our cases were two patients (male and female) with pre- and postnatal growth retardation, cutis laxa, characteristic facies and other manifestations which proved that they were affected with cutis laxa. their famil...

purpose: to evaluate the clinical manifestations and results of lensectomy in patients with hereditary lens subluxation at labbafinejad medical center, tehran-iran from 1996 t 2003. method: in an interventional case series, records of patients with hereditary lens subluxation who had undergone lensectomy were reviewed. patients with at least 6 months of follow up were included. background disea...

alport syndrome is a progressive hereditary nephritis leading to renal failure. nearly all of the documents declare that alport syndrome is inherited as x-linked dominant trait and reports of autosomal inheritance form is very rare. this paper presents an iranian large alport family with autosomal recessive inheritance. in our patients alport disease was confirmed with electron microscopic stud...

let $m$ be a right module over a ring $r$, $tau_m$ a preradical on $sigma[m]$, and$ninsigma[m]$. in this note we show that if $n_1, n_2in sigma[m]$ are two$tau_m$-lifting modules such that $n_i$ is $n_j$-projective ($i,j=1,2$), then $n=n_1oplusn_2$ is $tau_m$-lifting. we investigate when homomorphic image of a $tau_m$-lifting moduleis $tau_m$-lifting.

A Proportional-Integral-Derivative (PID) control is the most commonly used algorithm in industrial control systems. With its three term functionality providing regulation to both transient and steady state responses, PID control offers the simplest and most efficient solution to many industrial control problems. Tuning of PID gain parameters continuous to be important as these parameters has gr...

introduction: maxillary osteomyelitis is a rare phenomenon. if it occurs, evaluation for underlying disease especially osteopetrosis must be considered. osteomyelitis occurs as a complication in 10% of the cases of osteopetrosis. case report: this is a case report of maxillary osteomyelitis presented in a 15-year old boy with osteopetrosis.  in this case, the disease represented mainly with fac...

background: hereditary angioedema (hae) is a rare autosomal dominant primary immunodeficiency with complement system defect characterized by recurrent episodes of angioedema involving the skin or mucosa of the upper respiratory and gastrointestinal tracts. objective: to characterize the clinical and laboratory data of hereditary angioedema in iran. methods: patients with probable diagnosis of a...

hereditary spastic paraplegias are highly heterogeneous neurodegenerative disorders with some special mutations. we report on a patient with pescavus, distal a myotrophy, hyper extended fingers, and pectus excavatum. neurological examination showed that he had proximal lower limbs weakness with a positive gower sign, exaggerated lower limbs deep tendon reflexes with spasticity, distal muscle wa...

SPICE is a widely used tool for simulation of analog circuits. Accurate models of devices are crucial for obtaining realistic results from the simulation. Although SPICE provides circuit designers with built-in models for most widely used devices many devices still must be modelled with subcircuit models in order to achieve sufficient accuracy. The hardest part of creating a SPICE model for a p...