We report a rare case of solitary paraganglioma arising from the small bowel mesentery, found in 70-year-old female who presented with abdominal pain. Paragangliomas are neuroendocrine, neural crest-derived tumors, most commonly adrenal medulla. While extra-adrenal paragangliomas arise diverse locations, mesenteric origins extremely rare. Our comprehensive review shows 35 previously documented ...

UNLABELLED Composite pheochromocytoma/paraganglioma is a rare tumor with elements of pheochromocytoma/paraganglioma and neurogenic tumor. Most were located in the adrenal glands, and extra-adrenal composite pheochromocytoma is extremely rare. Only 4 cases in the retroperitoneum have been described in the online database PUBMED. Here, we report a case of retroperitoneal extra-adrenal composite p...

The 2004 WHO classification of endocrine tumors restricts the term ‘Pheochromocytoma’ (PHEO) to define a tumor arising from catecholamine producing chromaffin cells in the adrenal medulla which is also called ‘intra-adrenal’ paraganglioma (PGL). Closely related tumors of extra-adrenal sympathetic and parasympathetic paraganglia are classified as extra-adrenal PGL. Over the last decade, major ad...

BACKGROUND To determine whether MRI feature analysis can differentiate benign retroperitoneal extra-adrenal paragangliomas and schwannomas. METHODS The MRI features of 50 patients with confirmed benign retroperitoneal extra-adrenal paragangliomas and schwannomas were retrospectively reviewed by two radiologists blinded to the histopathologic diagnosis. These features were compared between two...

INTRODUCTION Myelolipomas are rare, benign tumors comprising mature adipose tissue and hematopoietic elements. The vast majority occur within the adrenal glands, but extra-adrenal myelolipomas have also been reported in the presacral region, retroperitoneum, mesentery, stomach, spleen, liver, mediastinum and lungs. Here, we present a case of primary myelolipoma occurring in an unusual site: the...

Myelolipomas are rare benign tumors often detected as adrenal masses. Extra-adrenal myelolipomas are encountered even more rarely. The rate of detection of these lesions is increasing with improved radiological techniques. Because of their localization and morphological similarities to well differentiated liposarcomas, extra-adrenal myelolipomas need to be differentiated from other aggressive n...