نتایج جستجو برای: ert

تعداد نتایج: 1495  

Journal: :JAMA 1995
R Vassilopoulou-Sellin

OBJECTIVE To determine whether estrogen replacement therapy (ERT) adversely affected outcome of breast cancer survivors. METHOD A prospective descriptive study of all breast cancer survivors who requested ERT because of intractable menopausal symptoms. All patients presented voluntarily as gynecological outpatients and were all given oral continuous opposed ERT: 20 premarin and medroxyprogest...

2017
Benedikt Schoser Deborah A Bilder David Dimmock Digant Gupta Emma S James Suyash Prasad

BACKGROUND Humanistic burden considers the impact of an illness on a patient's health-related quality of life (HRQoL), activities of daily living (ADL), caregiver health, and caregiver QoL. Humanistic burden also considers treatment satisfaction and adherence to treatment regimens. Pompe disease is an autosomal recessive, progressive, multisystemic neuromuscular disease. Approval of enzyme-repl...

Journal: :Journal of applied physiology 1997
E M Brooks A L Morgan J M Pierzga S L Wladkowski J T O'Gorman J A Derr W L Kenney

This investigation examined effects of chronic (>/=2 yr) hormone replacement therapy (HRT), both estrogen replacement therapy (ERT) and estrogen plus progesterone therapy (E+P), on core temperature and skin blood flow responses of postmenopausal women. Twenty-five postmenopausal women [9 not on HRT (NO), 8 on ERT, 8 on E+P] exercised on a cycle ergometer for 1 h at an ambient temperature of 36 ...

Journal: :Studies in health technology and informatics 2004
Michael J. Lincoln Steven H. Brown Viet N. Nguyen Tim Cromwell John S. Carter Mark Erlbaum Mark S. Tuttle

The Veterans Health Affairs (VHA) branch of the Department of Veterans Affairs has undertaken an Enterprise Reference Terminology (ERT). VHA, arguably the largest integrated healthcare provider in the United States, has completely computerized virtually all clinical transactions, including physician orders and documentation. The VA is now integrating its clinical records across hundreds of site...

Journal: :The Journal of clinical investigation 2008
Katherine P Ponder

Enzyme replacement therapy (ERT) for the lysosomal storage disease mucopolysaccharidosis I (MPS I) involves i.v. injection of alpha-l-iduronidase, which can be taken up by cells throughout the body. While a significant immune response to ERT has been shown in patients with MPS I, little is known about what effect anti-enzyme antibodies have on treatment efficacy. In this issue of the JCI, Dicks...

2017
Derralynn A Hughes Kathleen Nicholls Suma P Shankar Gere Sunder-Plassmann David Koeller Khan Nedd Gerard Vockley Takashi Hamazaki Robin Lachmann Toya Ohashi Iacopo Olivotto Norio Sakai Patrick Deegan David Dimmock François Eyskens Dominique P Germain Ozlem Goker-Alpan Eric Hachulla Ana Jovanovic Charles M Lourenco Ichiei Narita Mark Thomas William R Wilcox Daniel G Bichet Raphael Schiffmann Elizabeth Ludington Christopher Viereck John Kirk Julie Yu Franklin Johnson Pol Boudes Elfrida R Benjamin David J Lockhart Carrolee Barlow Nina Skuban Jeffrey P Castelli Jay Barth Ulla Feldt-Rasmussen

BACKGROUND Fabry disease is an X-linked lysosomal storage disorder caused by GLA mutations, resulting in α-galactosidase (α-Gal) deficiency and accumulation of lysosomal substrates. Migalastat, an oral pharmacological chaperone being developed as an alternative to intravenous enzyme replacement therapy (ERT), stabilises specific mutant (amenable) forms of α-Gal to facilitate normal lysosomal tr...

2017
Karolina M. Stepien Chris J. Hendriksz

BACKGROUND Fabry disease, an X-linked genetic condition, results from alpha-galactosidase deficiency and increased accumulation of glycosphingolipids in cardiovascular tissues. Clinical manifestation includes vasculature associated complications. Hyperlipidaemia is one of the cardiovascular risk factors however it has never been well defined in Fabry disease. Enzyme Replacement Therapy (ERT) is...

Journal: :international journal of endocrinology and metabolism 0
george papadimas uoywwvm~} of ou}woog{ohomvovsmu}ioone huw,dwsimeov ogdog}~ologmnmwiootiopis ital, 74, vas. sophias ave, greece +30-2107289152, [email protected]; uoywwvm~} of ou}woog{ohomvovsmu}ioone huw,dwsimeov ogdog}~ologmnmwiootiopis ital, 74, vas. sophias ave, greece +30-2107289152, [email protected] gerassimos terzis uoywwvm~} of ou}woog{ohomvovsmu}ioone

background pompe disease is an inherited metabolic disorder characterized by α-glycosidase deficiency, which leads to lysosomal glycogen accumulation in many different tissues. the infantile form is the most severe with a rapidly fatal outcome, while the late onset form has a greater phenotypic variability, characterized by skeletal muscle dysfunction and early respiratory involvement. bone min...

2016
Bouwien E. Smid Maria J. Ferraz Marri Verhoek Mina Mirzaian Patrick Wisse Herman S. Overkleeft Carla E. Hollak Johannes M. Aerts

BACKGROUND We retrospectively compared biochemical responses in type 1 Gaucher disease patients to treatment with glycosphingolipid synthesis inhibitors miglustat and eliglustat and ERT. METHODS Seventeen GD1 patients were included (n = 6 eliglustat, (two switched from ERT), n = 9 miglustat (seven switchers), n = 4 ERT (median dose 60U/kg/m). Plasma protein markers reflecting disease burden (...

Journal: :Circulation 2002
Akihiko Wakatsuki Yuji Okatani Nobuo Ikenoue Takao Fukaya

BACKGROUND Postmenopausal estrogen replacement therapy (ERT) has an antioxidant effect that opposes the oxidation of LDL particles. Oral ERT-induced increases in plasma triglyceride, however, decrease LDL particle size, which may counteract this antioxidant effect. Because transdermal ERT decreases plasma triglyceride, it may not decrease LDL particle size and may preserve estrogen's antioxidan...

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