Septo-optic dysplasia (SOD) or Morsier syndrome is a rare congenital malformation of infantile neurodevelopment with systemic anatomical and functional involvement. It characterized by optic nerve hypoplasia, midline brain malformation, hypothalamic-pituitary axis hypoplasia. The spectrum clinical manifestations very wide, from ophthalmological problems to endocrinological disorders that determ...

This paper presents an algorithm for near-real time registration of airborne video sequences with reference images from a different sensor type. Phase-correlation using Fourier-Melin Invariant (FMI) descriptors allow to retrieve the rigid transformation parameters in a fast and non-iterative way. The robustness to multi-sources images is obtained by an enhanced image representation based on the...

Les auteurs prcsentent deux 11ouveaux cas du syndrome associant le diabcte sucre juvenile it !'atro­phic optiquc. Ccs deux malades ages de dix et de quinzc ans avaient un retard statural. La premiere malade hospitalisee pour une mcgavessie est decedce dans le tableau de coma acidocctonique et d'Insuffi­s,rncc rcna!e. Dans la deuxicme observation, outre une sun.lite de perception decouvcrte it r...

Un enfant de 12 ans atteint d'un lymphome medias­tinal a ete hospitalise pour des manifestations neurolo­giques comportant: facies myasthenique, douleurs radi­culaires intenses, amyotrophie et diminution de la force musculaire au niveau des membres.  A l'examen du liquide cephalo-rachidien, ii existait une meningite neoplasique. Celle-ci a ete traitee par le methotraxate intra-rachidien parall...

Septo-optic dysplasia also referred to as de Morsier syndrome and is a disorder of early brain development. Three characteristic features are under development (hypoplasia) of the optic nerve, abnormal formation of structures along the midline of the brain (such as absence of septum pellucidum and corpus callosum dysgenesis) and pituitary hypoplasia. CASE REPORT Female, born at 40 weeks of gest...

Introduction: Literature regarding the different degrees of hearing loss in patients with Cornelia de Lange syndrome (CDLS) reports that half of the affected patients exhibit severe to profound sensorineural hearing loss. We present the first pre-school child with CDLS who underwent cochlear implantation for congenital profound sensorineural hearing loss.   Case Report: A 3-year-old boy with CD...

A prop-03 de la tetanie de l'cnfant: presentation de quelques cas, reYue de la. litterature.  Parmi les diverses etiologies de la tetanie in­fantile, le rachitisme et la malabsorption sont les causes les plus frequentes en Iran.  La tetanie s'observe plus volontiers au debut du rachitisme et dans des stades avances. Un seul cas de tetanie fut obse:rve chez un enfant de trois mo:is, ancien pre...