Twin pregnancies are at increased risk of complications and adverse outcome compared to singletons. A significant contribution to higher morbidity and mortality seen in monochorionic twins is made by cardiac complications. Abnormal cardiac development in monochorionic pregnancies can be divided into primary structural cardiac lesions (structural cardiac anomalies unrelated to the existence of T...

We report the case of a young girl with a mixed total anomalous pulmonary venous return (cardiac and supracardiac) treated sequentially by partial neonatal surgery, and then catheterization at age 19 with installation of an Amplatzer device as a treatment of the remaining anomaly. We describe the usefulness of magnetic resonance imaging in both the diagnosis and follow-up of this anomaly.

Ebstein's anomaly is a rare congenital malformation of the tricuspid valve, often associated with an atrial septal defect. Death occurs usually from cardiac arrhythmias. The successful use of a two-catheter technique for elective Caesarean section with extradural analgesia is described and the hazards associated with Ebstein's anomaly in pregnancy and anaesthesia are discussed.

In 68 patients with anorectal malformations cardiovascular anomalies (CVA) were seen in 15 and genitourinary (GU) anomalies in 30. CVA were more frequent (33%) whenever there was a GU anomaly. Ventricular septal defect was the most frequent lesion. All but 1 CVA occurred with type III anorectal malformation. The complexity of the cardiac lesion did not parallel that of the GU anomaly.

BACKGROUND Isolated intrapericardial LAA aneurysm is a rare cardiac anomaly which manifests with angina, dyspnea on exertion (DOE), systemic embolization, arrhythmia, and congestive heart failure. CASE REPORT A 30-year-old female and a 46-year-old male were referred for evaluation of abnormal cardiac contour on chest radiograph and echocardiographic findings and non-specific symptoms. Transes...

Introduction Ebstein’s anomaly is associated with a wide range of cardiac dysrhythmias, including presence of 1 or more accessory pathways. We present a case of a girl with Ebstein’s anomaly and symptomatic tachycardia. Electrophysiology study demonstrated a slow conducting decremental pathway as well as inducible antidromic reentrant tachycardia. Voltage mapping of the pathway potential was pe...

Duplication of the mitral valve is a rare congenital cardiac anomaly, only twenty instances having been previously reported. There are on record in addition two cases of triplication of the mitral valve, a condition presumably resulting from a similar defect in development. Duplication of the tricuspid valve also occurs, but less commonly than the mitral anomaly. This case is reported in order ...

Pulmonary atresia with ventricular septal defect (PA-VSD) with pulmonary arterial supply arising from the aorta representing large MAPCAs associated with a right sided aortic arch is an uncommon anomaly. Most of the patients succumb to severe respiratory compromise or congestive cardiac failure very early. We report the clinical details and imaging findings of a case of PA-VSD with a right side...

NOMALOUS inferior vena cava with azygos or hemiazygos continuation has been considered to be a very rare anomaly in the past. However, since the development of cardiac catheterization and angiocardiography, this congenital abnormality has been reported with increasing frequency. This anomaly is usually associated with other cardiovascular defect, and there are few reported cases without other m...

Ebstein’s anomaly is very rare (0.5 %) cardiac anomaly seen in patient of congenital rubella syndrome. Epidemiology and clinical data are lacking to guide management strategy. Congenital rubella syndrome is manifestation of rubella infection in foetus during period of embryogenesis. A verity of structural heart defect are known to occur with CRS but Ebstein’s anomaly has not been described in a...