OBJECTIVES Budd-Chiari syndrome is a rare and serious complication of Behçet's disease, and is the result of occlusion of the major hepatic veins, the adjacent inferior vena cava, or both. The aim of this study was to determine the prevalence, clinical and laboratory findings, and treatment and clinical course of Budd-Chiari syndrome associated with Behçet's disease. METHODS We analyzed retro...

the budd–chiari syndrome (bcs) is a rare disorder caused by the obstruction of the hepatic veins or the inferior vena cava (ivc) at the suprahepatic level. this syndrome is developed by either hepatic vein thrombosis or mechanical venous obstruction and leads to centrilobular hepatic congestion with the subsequent development of fibrosis and cirrhosis. intracardiac tumors have been rarely repor...

background: â budd-chiari syndrome (bcs) is a rare syndrome caused by hepatic venous outflow obstruction. the etiology of bcs differs between western and eastern countries. this article is a review of all published articles in iranian and international journals regarding different aspects of bcs (prevalence, etiology, and conventional treatments) in iran. materials and methods : â  in this revi...

Primary Budd-Chiari syndrome is related to thrombosis of hepatic veins or the terminal portion of the inferior vena cava. This rare disease is usually caused by multiple concurrent factors, including acquired and inherited thrombophilias. Half of the patients with primary Budd-Chiari syndrome are affected with a myeloproliferative disease, the recognition of which is largely based on the assess...

Paroxysmal nocturnal hemoglobinuria (PNH) is a progressive, life-threatening disorder characterized by chronic intravascular hemolysis caused by uncontrolled complement activation. Hepatic vein thrombosis (Budd-Chiari syndrome) is common in PNH patients. This case report describes the response to eculizumab (a humanized monoclonal antibody that inhibits terminal complement activation) in a 25-y...