نتایج جستجو برای: berardinelli

تعداد نتایج: 127  

Journal: :Indian Journal of Dermatology, Venereology, and Leprology 2011

Journal: :Archives of disease in childhood 1963
M A SALMON J N WEBB

This account by James Stephens (1912) of no less than six male leprechauns seen simultaneously has not been improved upon, for the medical literature to date includes descriptive accounts of only five examples of the rare syndrome of leprechaunism, and only one of these is male. Leprechaunism was first described by Donohue (1948) and later by Donohue and Uchida (1954), Evans (1955), Schaffer (1...

Journal: :The Journal of Cell Biology 2008
Weihua Fei Guanghou Shui Bruno Gaeta Ximing Du Lars Kuerschner Peng Li Andrew J. Brown Markus R. Wenk Robert G. Parton Hongyuan Yang

Lipid droplets (LDs) are emerging cellular organelles that are of crucial importance in cell biology and human diseases. In this study, we present our screen of approximately 4,700 Saccharomyces cerevisiae mutants for abnormalities in the number and morphology of LDs; we identify 17 fld (few LDs) and 116 mld (many LDs) mutants. One of the fld mutants (fld1) is caused by the deletion of YLR404W,...

Journal: :Journal of medical genetics 2002
L Van Maldergem J Magré T E Khallouf T Gedde-Dahl M Delépine O Trygstad E Seemanova T Stephenson C S Albott F Bonnici V R Panz J L Medina P Bogalho F Huet S Savasta A Verloes J J Robert H Loret M De Kerdanet N Tubiana-Rufi A Mégarbané J Maassen M Polak D Lacombe C R Kahn E L Silveira F H D'Abronzo F Grigorescu M Lathrop J Capeau S O'Rahilly

Generalised lipodystrophy of the Berardinelli-Seip type (BSCL) is a rare autosomal recessive human disorder with severe adverse metabolic consequences. A gene on chromosome 9 (BSCL1) has recently been identified, predominantly in African-American families. More recently, mutations in a previously undescribed gene of unknown function (BSCL2) on chromosome 11, termed seipin, have been found to be...

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