background cutis marmorata telangiectatica congenita (cmtc) is a sporadic congenital skin vascular abnormality. significant number of patients has other congenital anomalies. case report we report a case of a preterm male newborn with cutis marmorata pattern presented on the skin of the face, right side of front of the trunk, whole back, glutei and both legs. besides, microretrognatia and asymm...

ellis-van creveld sydrome (chondroectodermal dysplasia) is a hereditary form of short limb disproportionate dwarfism characterized by diffuse involvement of skeletal system and visceral organs. two brothers affected by this syndrome are presented here following a brief account of the disease's manifestations.

damage to essential facilities (e.g. lifelines and industrial facilities) due to extreme loads may cause remarkable indirect impact as well as direct physical loss. hence understanding seismic performance of essential facilities is very important in high seismic risk regions. on october 23, 2011 an earthquake of magnitude mw7.2 occurred in van province in eastern turkey. several damages occurre...

hypothyroidism is usually associated with delayed pubertal development but in rare occasions precocious puberty may ensue which is seen in cases of prolonged and untreated hypothyroidism. this is also called the van wyk grumbach syndrome. here we present 4 cases of precocious puberty due to hypothyroidism.

reaction mechanism among indoline-2,3-dione, pyrrolidine-2-carboxylic acid and (z)-2-(1-(2-hydroxynaphthalen-1-yl)ethylidene)hydroxycarboxamide to form 1’-((((aminooxy)carbonyl)amino)methyl)-2’-(1-hydroxynaphthalen-2-yl)-2’-methyl-1’,2’,5’,6’,7’,7a’-hexahydrospiro[indoline-3,3’-pyrrolo[1,2-a]imidazole-2-one was investigated using density functional theory (dft) at b3lyp basis theory. the three-...

ellis-van creveld syndrome is transmitted as an autosomal recessive trait. this syndrome is accompanied in 60% of cases with congenital heart disease, mostly single atrium or large asd. patients are mostly symptomatic, but in this rare case despite 68 years of age, the patient was free of symptoms except for complete heart block for which pacemaker was inserted

abstract water retention curve (wrc) is a fundamental property of soil. it is used to evaluate available water, permeability, drainage and movement of solutes. despite numerous studies on wrc of soils abroad, no local study has been carried out on charmahal-va-bakhtiari soils. the objective of this study was to compare the quality of fitting of several wrc models to lordegan soils and to select...

an earthquake was happened on 23 october 2011 in van, turkey (mw7.2) at the eastern most area of anatolian plateau and in the neighborhood of iranian border (west azerbaijan province). the study was performed based on field and office observations and has been focused on the process of disaster management in turkey after the 23 october 2011 earthquake. we surveyed the quake from the view point ...