نتایج جستجو برای: severe combined immunodeficiency

تعداد نتایج: 782574  

Journal: :Archives of Disease in Childhood 1982

Journal: :Japanese Journal of Clinical Immunology 1983

Journal: :Orphanet Journal of Rare Diseases 2017

Journal: :Acta biochimica et biophysica Sinica 2012
Maria P Limberis

Despite the first application of gene therapy in 1990, gene therapy has until recently failed to meet the huge expectations set forth by researchers, clinicians, and patients, thus dampening enthusiasm for an imminent cure for many life-threatening genetic diseases. Nonetheless, in recent years we have witnessed a strong comeback for gene therapy, with clinical successes in young and adult subj...

2017
Luiz Vicente Rizzo

aDirector of Research, Israelita Albert Einstein Hospital, São Paulo, SP, Brasil. Received on January 11, 2017. © 2017 Sociedade de Pediatria de São Paulo. Published by Zeppelini Publishers. This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/). EARLY DIAGNOSIS OF SEVERE COMBINED IMMUNODEFICIENCIES Diagnóstico precoce das imunodeficiências combinad...

2017
Rosanne Spolski Daniel Gromer Warren J Leonard

Interleukin (IL)-2, IL-4, IL-7, IL-9, IL-15, and IL-21 form a family of cytokines based on the sharing of a receptor component, the common cytokine receptor γ chain, γ c, which is encoded by the gene mutated in humans with X-linked severe combined immunodeficiency (XSCID). Together, these cytokines play critical roles in lymphoid development, differentiation, growth, and survival as well as med...

Journal: :Clinical infectious diseases : an official publication of the Infectious Diseases Society of America 2014
Akifumi Endo Ken Watanabe Tamae Ohye Kyoko Suzuki Tomoyo Matsubara Norio Shimizu Hiroki Kurahashi Tetsushi Yoshikawa Harutaka Katano Naoki Inoue Kohsuke Imai Masatoshi Takagi Tomohiro Morio Shuki Mizutani

It has been unclear whether chromosomally integrated human herpesvirus 6 (ciHHV-6) can be activated with pathogenic effects on the human body. We present molecular and virological evidence of ciHHV-6A activation in a patient with X-linked severe combined immunodeficiency. These findings have significant implications for the management of patients with ciHHV-6.

سخایی , ناهید, غفاری , جواد, مسیحا , فرزاد,

Ataxia-telangiectasia syndrome is an autosomal recessive associated with combined immunodeficiency, progressive cerebellum ataxia, telangiectasia, ocolomotor apraxia, dysartheria and respiratory infections. In this study we reported three cases from a family with classical symptoms. Second sibling was died at 13 old years because severe respiratory infection but third and forth siblings have ...

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