BACKGROUND Fetal unilateral lung agenesis, complicated with cardiac shifting, is a rare anomaly, the diagnosis of which remains a challenge for many sonographers in routine screening programs. The present study describes a systematic approach for the diagnosis of fetal unilateral lung agenesis and cardiac malpositions in routine prenatal screening. METHODS A total of 18 cases of fetal unilate...

Congenital pulmonary artery agenesis is a rare cardiovascular malformation, frequently oligosymptomatic,1,2 that can be complicated with unilateral pulmonary edema3 or pulmonary hypertension.1,2,4 We report the case of a patient with congenital pulmonary artery agenesis and pulmonary hypertension who developed unilateral pulmonary edema and discuss the role of sildenafil in pulmonary hypertensi...

Isolated unilateral absence of pulmonary artery (UAPA) is a rare congenital anomaly. When detected in infancy, the condition is commonly associated with cardiovascular defects which are more frequently associated with left pulmonary artery agenesis. Patients with isolated right pulmonary artery agenesis survive into adulthood with minimal or no symptoms and are diagnosed incidentally on the che...

Abstract Pulmonary agenesis is a rare malformation associated with congenital heart disease and may lead to life-threatening condition death without pre-planned surgical medical support. We report an unusual case of unilateral pulmonary in combination total anomalous venous connection, complete vascular ring, retroaortic, retroesophageal innominate vein, secondary atrial septal defect, which wa...

BACKGROUND Bilateral pulmonary agenesis is a rare congenital anomaly incompatible with life that can be missed on routine prenatal screening. Prenatal ultrasound diagnosis of this fatal anomaly can aid in prenatal counseling and postdelivery care. CASE STUDY We report the case of a newborn who was born prematurely at 29 weeks gestation and underwent several unsuccessful intubation attempts im...

Congenital pulmonary agenesis is a rare condition which poses diagnostic difficulties. More than 50% of these patients die before the first five years of life. Few patients may remain asymptomatic throughout their life. We report a case of a two month old male infant with right pulmonary agenesis who presented with severe respiratory distress in whom a diagnosis was made following computed tomo...

Congenital pulmonary artery agenesis is a rare cardiovascular malformation, frequently oligosymptomatic,1,2 that can be complicated with unilateral pulmonary edema3 or pulmonary hypertension.1,2,4 We report the case of a patient with congenital pulmonary artery agenesis and pulmonary hypertension who developed unilateral pulmonary edema and discuss the role of sildenafil in pulmonary hypertensi...