نتایج جستجو برای: pantothenate kinase associated neurodegeneration

تعداد نتایج: 1714897  

Journal: :Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques 2019

Pantothenate kinase- associated neurodegeneration (PKAN) syndrome is a rare autosomal recessive disorder characterized by progressive extrapyramidal dysfunction and iron accumulation in the brain and axonal spheroids in the central nervous system. It has been shown that the disorder is caused by mutations in PANK2 gene which codes for a mitochondrial enzyme participating in coenzyme A biosynthe...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2010
Anil Rana Erwin Seinen Katarzyna Siudeja Remco Muntendam Balaji Srinivasan Johannes J van der Want Susan Hayflick Dirk-Jan Reijngoud Oliver Kayser Ody C M Sibon

Pantothenate kinase-associated neurodegeneration (PKAN), a progressive neurodegenerative disorder, is associated with impairment of pantothenate kinase function. Pantothenate kinase is the first enzyme required for de novo synthesis of CoA, an essential metabolic cofactor. The pathophysiology of PKAN is not understood, and there is no cure to halt or reverse the symptoms of this devastating dis...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید