OBJECTIVES We examined the long-term effects of everolimus in patients with renal angiomyolipoma associated with tuberous sclerosis complex or sporadic lymphangioleiomyomatosis. METHODS Following favorable results from the double-blind core phase of EXIST-2 (NCT00790400), patients were allowed to receive open-label everolimus (extension phase). Patients initially randomly assigned to everolim...

PURPOSE We reviewed our experience with fat poor cases of angiomyolipoma. MATERIALS AND METHODS The records of patients with angiomyolipoma, as determined by pathological study, from 1998 to 2004 were reviewed by recording patient demographics and outcomes. Fat poor cases were defined as the failure of imaging to demonstrate fat in a lesion. Computerized tomography and histological characteri...

INTRODUCTION A hepatic angiomyolipoma is a rare benign tumor of the liver composed of a mixture of smooth muscle cells, blood vessels and a variable amount of adipose tissue. Differentiating them from malignant liver tumors can often be very difficult. CASE PRESENTATION We report the case of a 43-year-old Caucasian man presenting with a large liver mass in the right lobe. The results of magne...

Renal angiomyolipoma is a benign clonal neoplasm that consists of three constituents, namely, blood vessels, adipose tissue and smooth muscle. Although renal angiomyolipoma has a benign nature and grows slowly, extrarenal occurrences have been reported in the hilar lymph nodes, retroperitoneum, liver, colon and direct extension to the renal vein and inferior vena cava as a tumor thrombus. Such ...

OBJECTIVE To describe a case of renal angiomyolipoma treated by robotic assisted surgery. METHOD AND RESULTS We report the case of a 26 year old females patient, in the context of third month pregnancy, who was diagnosed of spontaneous self-limited retroperitoneal hemorrhage due to renal angiomyolipoma. The patient was treated conservatively until normal delivery. At the 3rd month postpartum ...

Extrarenal angiomyolipoma (AML) is an extremely uncommon lesion, accounting for less than 9% of all angiomyolipomas. We present a previously unreported case of a rarely located gigantic extrarenal angiomyolipoma at the posterolateral chest wall of a 35-year-old woman. Clinically, the lesion had all the characteristics of a benign tumor, being soft in palpation, painless, and growing in size in ...

A 60-year-old male patient presented with complaints of loss of appetite and bloated abdomen of two weeks duration. The radiological examination revealed large mass involving left kidney. With a clinical and radiological diagnosis of renal cell carcinoma, radical nephrectomy was done. Histopathological examination revealed a neoplasm composed purely of epithelioid cells. Based on histopathologi...

Angiomyolipoma is a common tumor of the kidney but has rarely been found in the mediastinum. We report a case of angiomyolipoma of the posterior mediastinum in a 62-year-old woman. She experienced exertional dyspnea and intermittent cough at admission. Computed tomography indicated a tumor located at the left paravertebral and upper posterior mediastinum and MRI imaging demonstrated a mass with...

Adrenal angiomyolipoma is rare. Only four cases have been reported so far. These are commonly found in Kidney but extrarenal sites are also mentioned. Angiomyolipoma arising in adrenal is very rare entity, usually asymptomatic, diagnosed incidentally on radiological investigation of abdomen for other conditions. We report our experience with a 45-year-old woman who presented with epigastric dis...

Tumor rupture with hemorrhage is a severe complication of renal angiomyolipoma. Urgent transcatheter arterial embolization is an effective method for the patient suffering from life-threatening hemorrhage due to ruptured angiomyolipoma. Elective surgery has been suggested because of the possibility of rebleeding or abscess formation after embolization. However, it is not easy to perform a nephr...