A middle-aged woman was admitted to hospital after a motor vehicle accident. A large acute intracranial haematoma was initially thought to be traumatic in origin, but its unusual position and the lack of external features of head trauma prompted investigation for other causes of intracerebral haemorrhage. Moyamoya intracranial vascular abnormalities were diagnosed. We discuss the presentation o...

OBJECTIVE Moyamoya is a progressive arteriopathy that predisposes patients to stroke due stenosis of the intracranial internal carotid arteries and their proximal branches. Despite morbidity caused by this condition, ability accurately predict prognosis for individual remains challenging. The goal study was develop systematic scoring method based on parenchymal findings preoperative brain MRI l...

We present the case of a 29-year-old woman with Down syndrome who developed bilateral frontal ischemic stroke. Cerebral angiography demonstrated an occlusion of the both supraclinoid internal carotid arteries associated with dilated collateral vessels, consistent with moyamoya disease. We review the clinical and radiological features of moyamoya disease associated with Down syndrome and discuss...

OBJECTIVES This study was undertaken to describe the clinical, radiologic, and angiographic features of moyamoya syndrome in a surgical series of children and adults with Down syndrome. We wished to define the features of moyamoya syndrome associated with Down syndrome and to determine the results of surgical revascularization among these patients at early and late follow-up times. METHODS We...

BACKGROUND AND PURPOSE Moyamoya syndrome is an uncommon chronic occlusive cerebrovascular disease in children. The origin of moyamoya syndrome remains undetermined. The role of the prothrombotic disorders contributing to its pathogenesis has not been completely elucidated. The purpose of this study was to determine the frequency of prothrombotic disorders in a pediatric population with moyamoya...

Moyamoya Disease and Syndrome are neurological conditions that affect the blood vessels in brain, characterized by progressive stenosis of terminal portion internal carotid artery its main branches, consequent network collateral at base skull whose angiographic pattern simulates a "smoke cloud". Both have universal distribution, although is more frequently seen Asian population. The term "Moyam...

Moyamoya disease is an idiopathic progressive steno-occlusive disorder of the intracranial arteries located at the base of the brain. It is associated with the development of compensatory extensive network of fine collaterals. Moyamoya disease is considered syndromic when certain genetic or acquired disorders such as polycystic kidney disease, neurofibromatosis, or meningitis are also present. ...

Moyamoya angiopathy is characterized by a progressive stenosis of the terminal portion of the internal carotid arteries and the development of a network of abnormal collateral vessels. This chronic cerebral angiopathy is observed in children and adults. It mainly leads to brain ischemic events in children, and to ischemic and hemorrhagic events in adults. This is a rare condition, with a marked...

Down syndrome, the most common chromosomal abnormality, may be associated with various neurologic complications such as moyamoya syndrome, cervical spinal cord compression due to atlantoaxial subluxation, and basal ganglia damage, as well as epileptic seizures and stroke. Many cases of Down syndrome accompanied by isolated neurologic manifestations have been reported in children; however, Down ...