As an idiopathic interstitial pneumonia, desquamative interstitial pneumonia (DIP) is an uncommon form of interstitial lung disease and is considered to be a smoking- or dust inhalation-related interstitial pneumonia in the majority of cases. However, the details regarding immunoglobulin G4 (IgG4)-related lung disease remain unclear and controversial. We herein report the first case of DIP comp...

Definition: Interstitial lung disease (ILD) refers to a broad range of conditions that have common clinical, physiological, and radiological features. ILD is not one disease, but several diseases that do not necessarily share a common histopathological or pathophysiological basis. By strict definition, ILD involves abnormalities of the interstitium, the potential space between the epithelial an...

Interstitial lung disease is the collective name given to over 200 different types of parenchymal lung disorders (Demedts et al, 2001) (these are disorders that affect the functioning parts of an organ — in this case the lungs — as opposed to the structural elements, such as connective tissue etc). They are different from the more common respiratory diseases such as chronic obstructive pulmonar...

Occupational interstitial lung diseases are a diverse group of disorders of varied cause. Occupational causes account for a significant portion of all interstitial lung diseases, and new causes continue to be described. Although some are diseases of antiquity, they continue to occur in the workplace and often are misdiagnosed as "idiopathic" when physicians miss the connection to past-inhaled e...

BACKGROUND Interstitial lung disease encompasses a diverse group of chronic lung conditions characterised by distressing dyspnoea, fatigue, reduced exercise tolerance and poor health-related quality of life. Exercise training is one of the few treatments to induce positive changes in exercise tolerance and symptoms, however there is marked variability in response. The aetiology and severity of ...

Systemic sclerosis, or scleroderma, is a collagen vascular disease characterized by hardening of the skin and involvement of internal organs, most commonly the esophagus. The most frequent cause of death in these patients is lung disease. Esophageal dysfunction has been implicated in the pathogenesis of interstitial lung disease. We previously developed a standard for the esophageal diameter on...

Because the list of interstitial lung diseases is so extensive, encompassing more than 180 chronic lung diseases in which the interstitium is altered by inflammation and/or fibrosis, this chapter focuses on several inflammatory lung diseases of unknown etiology: usual interstitial pneumonitis, respiratory bronchiolitis, idiopathic bronchiolitis obliterans with organizing pneumonia, pulmonary La...

Interstitial lung disease (ILD) in children (chILD) is very different in many aspects to the adult disease. First, chILD is rare, estimated at 0.36 per 100,000, compared with 60– 80 per 100,000 for ILD in adults [1]. Secondly, the spectrum of conditions, in particular in infancy, is much wider than in adults. The conditions encompass growth and developmental issues, as well as immunological pro...

Interstitial lung diseases are a group of diffuse parenchymal lung disorders associated with substantial morbidity and mortality. Knowledge achieved in recent years has resulted in the publication of the new classification of idiopathic interstitial pneumonias, according to which there are three groups: major, rare and unclassified. The novelty of the new classification comes from the fact that...