A 6-year-old girl with Down syndrome was referred to our team for joint management. She was having severe speech and language difficulties. Her hearing was assessed, and the pure tone audiometry showed a moderate conductive hearing loss (40 dB) in the left ear and profound hearing loss in the right ear. A CT scan and MRI of temporal bone (Figs. 1 and 2) revealed a hypodense mass in the left tym...

Mondini dysplasia is a congenital malformation of the inner ear, which is characterized by a short and large cochlear canal of 1.5 turn rather than 2.5 turns and an apical region with cystic dilatation. Patients present with congenital deafness, when both cochlea are affected. Unilateral disease may cause recurrent meningitis, otorrhea or rhinorrhea. In this article, we report a three-year-old ...

Introduction: Sensorineural hearing loss (SNHL) is one of the possible complications of radiotherapy treatment of brain tumors. The auditory system of patients with brain tumors often is placed inside of radiation field and receives a significant amount of radiation dose resulting in hearing loss. The purpose of this study was to compare contouring and delivery dose to cochlea...

Recent developments in medicine have given us a better insight into a group of disorders known as autoimmune diseases. In particular, advances have occurred in our understanding of the Autoimmune Inner Ear Disease (AIED). In this article, the authors review the different postulated theories in the pathogenesis of this disease. The clinical presentation, the available para-clinical diagnostic to...

background many clinical and experimental studies have been done to analyze the anatomical and functional aspects of the internal auditory canal (iac) in human beings since there are great inter-individual variability and structural variations that may occur regarding the other adjacent structures. objectives the purpose of this study was to characterize the morphology of the internal auditory ...

BACKGROUND AND PURPOSE Intracranial lipomas are uncommon congenital malformations that most often are asymptomatic. A rare subset of intracranial lipomas arises within the vestibule of the inner ear, which can cause sensorineural hearing loss. We present the CT and MR imaging characteristics of lipomas within the vestibule of the inner ear and propose a pathogenetic mechanism for this malformat...