نتایج جستجو برای: hydrops fetalis

تعداد نتایج: 1807  

2016
Bariha Kalpana

Incidence of immune hydrops fetal is decreasing with the liberal use of anti-D immunoglobulin, But this condition has not been eradicated. We report here a case of immune hydrops fetalis detected on ultrasonography.

Journal: :Archives of disease in childhood 1994
C K Phoon

Non-immune hydrops fetalis is a relatively rare and complex disorder that requires detailed investigation and coordinated management by a multidisciplinary team. There is a lack of clear advice in the literature on the immediate management and investigation of neonatal hydrops. The approach described here has been used in our unit and has been welcomed, particularly by resident staff. Hydrops f...

Journal: :Revista do Hospital das Clinicas 2003
Renata Suman Mascaretti Mário Cícero Falcão Andrea M Silva Flávio Adolfo Costa Vaz Cléa Rodrigues Leone

PURPOSE To determine the incidence and characteristics of nonimmune hydrops fetalis in the newborn population. METHOD A retrospective study of the period between 1996 and 2000, including all newborns with a prenatal or early neonatal diagnosis of nonimmune hydrops fetalis, based on clinical history, physical examination, and laboratory evaluation. The following were analyzed: prenatal follow-...

Journal: :Clinical chemistry 2007
Sherry Sze Yee Ho Samuel S Chong Evelyn S C Koay Yiong Huak Chan Ponnusamy Sukumar Lily-Lily Chiu Wen Wang Ashim Roy Mary Rauff Lin Lin Su Arijit Biswas Mahesh Choolani

BACKGROUND We sought to develop a rapid prenatal diagnostic test for simultaneous detection of HbBarts hydrops fetalis and exclusion of maternal contamination. METHODS We developed a multiplex quantitative fluorescent PCR (QF-PCR) test that detects the presence/ absence of 2 microsatellite markers (16PTEL05/16PTEL06) located within breakpoints of the Southeast Asia ((-SEA)) deletion. HbBarts ...

2010
Hasan Kafali Yüksel Arıkan Onaran Esra Keskin Umut Sari Ismail Kirbas

Ballantyne’s syndrome has originally been described for hydrops fetalis, which is associated with rhesus isoimmunization; however, hydrops fetalis can also occur in association with non-immunological causes, including Ebstein’s anomaly, Galen’s vein aneurysm, fetal arrhythmias, and sacrococcygeal teratoma (SCT). SCT is the most commonly presenting tumor in newborn babies, occurring in approxima...

2012
Wen Wang Christine H.A. Yap Seong Feei Loh Arnold S.C. Tan Mui Nee Lim Ethiraj B. Prasath Melinda L.H. Chan Wei Chin Tan Boran Jiang Gare Hoon Yeo Joyce Matthew Angela Ho Sherry S.Y. Ho Peng Cheang Wong Mahesh A. Choolani Samuel S. Chong

The high incidence of double-gene deletions in α-thalassemia increases the risk of having pregnancies with homozygous α0-thalassemia, the cause of the lethal hemoglobin (Hb) Bart’s hydrops fetalis syndrome. Preimplantation genetic diagnosis (PGD) has played an important role in preventing such cases. However, current gap-PCR based PGD protocol for deletional α-thalassemia required specific prim...

2014
Paul Singh Cristiano Jodicke Tara Swanson Dev Maulik

Introduction Most often, ganglioneuromas affect older pediatric and adult patients. They are typically slow growing tumors that remain clinically silent until they become large enough to cause symptoms by compression of adjacent structures. Case We report a case of a 22-year-old Hispanic gravida 2 para 1 female patient who was found to have massive hydrops fetalis at 20 completed gestational we...

2016
Adriana M Montaño Ngu Lock-Hock Robert D Steiner Brett H Graham Marina Szlago Robert Greenstein Mercedes Pineda Antonio Gonzalez-Meneses Mahmut Çoker Dennis Bartholomew Mark S Sands Raymond Wang Roberto Giugliani Alfons Macaya Gregory Pastores Anastasia K Ketko Fatih Ezgü Akemi Tanaka Laila Arash Michael Beck Rena E Falk Kaustuv Bhattacharya José Franco Klane K White Grant A Mitchell Loreta Cimbalistiene Max Holtz William S Sly

BACKGROUND Mucopolysaccharidosis VII (MPS VII) is an ultra-rare disease characterised by the deficiency of β-glucuronidase (GUS). Patients' phenotypes vary from severe forms with hydrops fetalis, skeletal dysplasia and mental retardation to milder forms with fewer manifestations and mild skeletal abnormalities. Accurate assessments on the frequency and clinical characteristics of the disease ha...

2013
Ercan Tutak Ayla Eker Sarıboyacı Altuğ Semiz Necip Cihangir Yılanlıoğlu Cem Kara

Sum mary Sialidosis is a rare congenital lysosomal storage disease with autosomal recessive transmission caused by a deficiency of alpha-N-acetylneuraminidase (sialidase). The findings begin in the intrauterine period in congenital type of sialidosis and the cases die in the postnatal period due to hydrops fetalis with multiorgan failure. Here, a case of premature baby born to a consanguineous ...

2016
Silvia Martin-Almedina Ines Martinez-Corral Rita Holdhus Andres Vicente Elisavet Fotiou Shin Lin Kjell Petersen Michael A. Simpson Alexander Hoischen Christian Gilissen Heather Jeffery Giles Atton Christina Karapouliou Glen Brice Kristiana Gordon John W. Wiseman Marianne Wedin Stanley G. Rockson Steve Jeffery Peter S. Mortimer Michael P. Snyder Siren Berland Sahar Mansour Taija Makinen Pia Ostergaard

Hydrops fetalis describes fluid accumulation in at least 2 fetal compartments, including abdominal cavities, pleura, and pericardium, or in body tissue. The majority of hydrops fetalis cases are nonimmune conditions that present with generalized edema of the fetus, and approximately 15% of these nonimmune cases result from a lymphatic abnormality. Here, we have identified an autosomal dominant,...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید