A triad of symptoms of varying degrees of dwarfism, hepatomegaly and obesity, developing slowly in diabetic children, has been commonly designated the Mauriac syndrome, after P. Mauriac's first descriptions published in 1930 and 1934'. Mauriac wrote that with the discovery of insulin a new disease was born: juvenile diabetes, with curious troubles and manifestations of endocrine disturbances no...

D. Mella-Flores, S. Mazard, F. Humily, F. Partensky, F. Mahé, L. Bariat, C. Courties, D. Marie, J. Ras, R. Mauriac, C. Jeanthon, E. M. Bendif, M. Ostrowski, D. J. Scanlan, and L. Garczarek CNRS/INSU, Observatoire Océanologique de Roscoff, UMR 7144, Groupe Plancton Océanique, 29680 Roscoff, France UPMC-Université Paris 06, Station Biologique, Place Georges Teissier, 29680 Roscoff, France School ...

Result A 5 year and 10 month old boy, was admitted with protuberant abdomen since one year ago. He had been recognized as type 1 DM and treated by subcutaneous insulin 4-5 U/day twice a day until admission. His abdomen became larger, wasted arms and legs so he couldn’t support his body, and just laid down for 3 months. He had retarded growth and development. Oedema face, chest was normal, diste...