Background: Treating a chronic disease such as hemophilia is to improve the symptoms and quality of life (QOL) of the patients. This study aimed to study the quality of life among hemophilic children and compare the quality of life between patients receiving prophylactic or on demand treatments. Materials and Methods: In this descriptive-comparative study, we enrolled 60 patients from three ...

Hemophilia is a disease of blood coagulation inherited as a sex linked recessive. The disorder is attributed to decreased blood levels of procoagulant factor VIII. However, mild forms of the disease with almost inapparent clotting defects have been reported. Patients with hemophilia often give a history of unusual bleeding associated with minor trauma. The disease may however remain undetected ...

background: treating a chronic disease such as hemophilia is to improve the symptoms and quality of life (qol) of the patients. this study aimed to study the quality of life among hemophilic children and compare the quality of life between patients receiving prophylactic or on demand treatments. materials and methods: in this descriptive-comparative study, we enrolled 60 patients from three mai...

The concept of risk factors in cardiovascular disease (CVD) has been well established. Smoking, hypertension, obesity, hypercholesterolemia, diabetes mellitus, and a positive family history for CVD are all associated with an increased risk of morbidity and mortality because of CVD. A prothrombotic state also contributes to the development of CVD. Increased levels of fibrinogen, von Willebrand f...

Hemophilia is the most common of the severe bleeding disorders and if not properly managed since early infancy can lead to chronic disease and lifelong disabilities. However, it enjoys the most efficacious and safe treatment among the most prevalent monogenic disorders. Hemophilia should be considered in the neonatal period in the case of unusual bleeding or in the case of positive family histo...

Two unrelated families are described with mild hemophilia A in whom six obligate carriers had unusually low VIII AHF levels. In each family, successive generations of males were affected with hemophilia A as determined by low VIII AHF in the presence of normal VIII AGN and VIII VWF levels. In the first family, two of five obligate carriers had low VIII AHF levels associated with clinical bleedi...

background: pain, as a crucial subsequence of joint hemorrhages in hemophilia patients, is chronic, debilitating, and distracting. this study aimed to describe and interpret pain experiences of hemophilia patients in their lives. methods: this qualitative study with hermeneutic phenomenological approach was conducted on fourteen hemophilia patients who had been referred to a hemophilia center a...