نتایج جستجو برای: creutzfeldt
تعداد نتایج: 3390 فیلتر نتایج به سال:
OBJECTIVE To report the clinical, neuropsychological, linguistic, imaging, and neuropathological features of a unique case of sporadic Jakob-Creutzfeldt disease in which the patient presented with a logopenic variant of primary progressive aphasia. DESIGN Case report. SETTING Large referral center for atypical memory and aging disorders, particularly Jakob-Creutzfeldt disease. PATIENT Pat...
OBJECTIVES During an epidemiological study of Creutzfeldt-Jakob disease in Germany, Hashimoto's encephalitis was encountered as a differential diagnosis, which has not yet been described in this context. METHODS The symptoms and findings of seven patients who fulfilled the criteria for "possible" Creutzfeldt-Jakob disease are presented. RESULTS A Hashimoto's thyroiditis with antibodies agai...
Cohen D, Kutlay E, Edwards J, Peltier A, Beydoun A. Sporadic Creutzfeldt–Jakob disease presenting with nonconvulsive status epilepticus. Epil Behav 2004;5:792–6. Fernandez-Torre JL. Nonconvulsive status epilepticus in Creutzfeldt– Jakob disease. Clin Neurophysiol 2006;117:1879–80. Hirsch LJ, Claassen J, Mayer SA, Emerson RG. Stimulus-induced rhythmic, periodic, or ictal discharges (SIRPIDs): a ...
Four members of a kindred wi th Creutzfeldt-Jakob disease are reported, i n whom myoclonus d id not develop and in whom serial electroencephalograms performed late in their illness failed to show periodic sharp wave complexes. Otherwise, the patients’ disease duration, clinical features, and neuropathological findings were similar to those described in sporadic cases of Creutzfeldt-Jakob diseas...
BACKGROUND The objective of this study was to describe the diagnostic panorama of human transmissible spongiform encephalopathies across 11 countries. METHODS From data collected for surveillance purposes, we describe annual proportions of deaths due to different human transmissible spongiform encephalopathies in eleven EUROCJD-consortium countries over the period 1993-2002, as well as variat...
A 52 year old man with Creutzfeldt-Jakob disease who received a cadaveric dura mater graft 99 months before the onset is reported. The prion protein gene was homozygous for methionine at the polymorphic codon 129. Neuropathological examination disclosed a panencephalopathic type of Creutzfeldt-Jakob disease which was characterised by severe involvement of the cerebral white matter and cerebellu...
Three cases of probable iatrogenic transmission of Creutzfeldt-Jakob disease by neurosurgery are detailed together with a cluster of three cases in Eastern England possibly connected by dental procedures, and the development of Creutzfeldt-Jakob disease in a patient who had been in social contact with a familial case.
A periodic EEG pattern very similar to the changes in Creutzfeldt-Jakob disease was seen in a case of anoxic encephalopathy. Necropsy revealed status spongiosus of the cerebral cortex. Generalised repetitive sharp transients in anoxic encephalopathy occur when the patient is comatose and carry a poor prognosis. They are not specific for Creutzfeldt-Jakob disease.
Creutzfeldt-Jakob disease is a fatal spongiform encephalopathy, which typically presents with a rapidly progressing dementia and additional neurological findings that can be quite variable and diverse. Here we report the unusual case of a patient who presented with left alien limb sign without overt cognitive impairment and was ultimately diagnosed with pathologically confirmed Creutzfeldt-Jako...
OBJECTIVE To determine the strength of association between history of blood transfusion and development of Creutzfeldt-Jakob disease. DATA SOURCES English and non-English language articles published from January 1966 to January 1999 were retrieved using a keyword search of Medline and Embase. These were supplemented by handsearching key journals and searching bibliographies of reviews. STUD...
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