BACKGROUND Latent nystagmus is a horizontal binocular oscillation that is evoked by unequal visual input to the 2 eyes. It develops primarily in humans with congenital esotropia. OBJECTIVE To investigate the interrelationship between latent and peripheral vestibular nystagmus and their corollary neuroanatomical pathways. METHODS Examination of subcortical neuroanatomical pathways producing ...

A severe defect of optokinetic nystagmus (OKN) was found in 46 patients with congenital nystagmus. Abnormal patterns of OKN, such as superimposition of pendular oscillations on the optokinetic slow component and inversion of OKN, were observed. Optokinetic gain (eye movement velocity/drum velocity) was decreased compared to that in normal subjects, and optokinetic after-nystagmus, or transient ...

OBJECTIVE We wished to determine the effectiveness of horizontal rectus tenotomy in changing the nystagmus of patients with congenital nystagmus and, secondarily, how their visual function changed. DESIGN This was a prospective, noncomparative, interventional case series. PARTICIPANTS Ten adult patients with varied associated sensory defects and oculographic subtypes of congenital nystagmus...

대한신경과학회지 22권 5호 548 Periodic alternating nystagmus (PAN) is a rare type of spontaneous horizontal nystagmus, characterized by periodical reverse of direction with a transition period in between. PAN can occur in both congenital and acquired forms. We report a patient with acquired PAN associated with meningoencephalitis. To our knowledge, only a case of congenital PAN has been previously report...

Uniform field temporal contrast sensitivity functions were compared for 10 subjects with congenital nystagmus (seven idiopathic, three with albinism) and 10 normal observers. Sensitivity to luminance modulation did not differ significantly from normal at any temporal frequency tested except 0.5 Hz, at which the subjects with nystagmus had slightly higher sensitivity. In conjunction with other r...

Suppression of congenital nystagmus by eyelid closure was studied by electrooculography in four cases under various conditions in order to elucidate whether the suppression is caused by blocking of fixation or not. The nystagmus persisted in the light as well as in the dark provided that the eyes were kept open. Frenzel's glasses did not suppress the nystagmus except for one case in whom jerky ...

The cases presented are rare examples of congenital nystagmus associated with isolated absence of the optic chiasm. MR imaging in both patients demonstrated unremarkable anterior optic pathways and optic tracts. No additional midline central nervous system abnormalities, migrational anomalies, space-occupying lesions, or destructive processes were noted. These cases demonstrate that the achiasm...

Basal encephalocele is a rare craniofacial anomaly. In the present paper we report a 10-year-old boy presented with cleft palate, congenital nystagmus, and hypertelorism. During preoperative evaluation for cleft palate repair, a pulsatile mass was detected in the pharynx. Magnetic resonance imaging showed sphenoethmoidal type of basal encephalocele and agenesis of corpus callosum. Neurosurgical...