Pentalogy of Cantrell is a rare congenital abnormality. Even with high-quality medical care and staged corrective surgeries in professional hospitals, the mortality rate still very high long-term prognosis poor. Survival largely determined by complexity severity cardiac abnormalities, efficiency abdominal wall closure postoperative complications. A 24-year-old male patient complete pentalogy wa...

background: delayed or missed diagnosis of critical and cyanotic congenital heart disease (chd) in asymptomatic newborns may result in significant morbidity and mortality. the aim of this study was to determine the accuracy of pulse oximetry screening  performed on the first day of life for the early detection of critical and cyanotic chd in apparently normal newborns. methods: this cross-secti...

introduction: along with advances occurring in cardiopulmonary bypass (cpb) including improved anesthesia intubation and early surgical interventions, it has become possible to correct life-threatening congenital heart anatomic abnormalities in patients. our study aimed to collect information from one of the most important centers of pediatric cardiac surgery in iran since there is limited info...

Quadricuspid aortic valve (QAV) is a rare congenital cardiac entity. The recognition of QAV has clinical significance because QAV causes aortic valve dysfunction, commonly aortic regurgitation. QAV is often associated with other congenital cardiac abnormalities. Our case represents, to the best of our knowledge, the first reported case of QAV with a non-obstructive sub-aortic membrane.

introduction:patients with cyanotic heart disease may have an acceptable quality of life. however, they are invariably prone to several complications. the aim of this study is search about hematologic abnormalities in cyanotic congenital heart disease patients. materials and methods:  in this cross sectional study every cyanotic congenital heart disease patients who was referred to the adult co...

objective(s) carbamazepine (cbz) is an antiepileptic drug that is used widely for the treatment of epileptic seizures. neural tube defects (ntds), growth retardation, and nail hypoplasia are the most common features of teratogenic effects of this drug. the purpose of this study was to examine the effect of vitamin b6 on the developmental toxicity of cbz on mice. materials and methods sixty balb...

the ribs are essential structures of the osseous thorax that provide certain significant information and aid interpretation of radiologic images in daily routine practice. intrathoracic rib is a rare congenital anomaly that is usually discovered incidentally, but may cause in vain interventions in case of being unaware. we herein report an intrathoracic rib in a girl whose chest x-ray was stran...

large intercoronary communications in the absence of obstructive coronary artery disease constitute a very rare coronary artery anomaly in which there is a readily visible connection between the 2 coronary arteries with a unidirectional or bidirectional blood flow; consequently, this anomaly may be misinterpreted as a functioning collateral vessel, indicative of an unrecognized proximal coronar...

INTRODUCTION We propose to demonstrate that it is possible to implement a valid (diagnostic sensitivity for major cardiac malformations 90%), and universal (applied to over 90% of pregnant women), prenatal screening method for congenital heart defects. MATERIALS AND METHODS Prospective study. A total of 12478 pregnant women were evaluated between January 2008 and December 2010. Congenital hea...