نتایج جستجو برای: clinical exome sequencing

تعداد نتایج: 1271061  

Journal: :acta medica iranica 0
sima shokri department of allergy and clinical immunology, rasool-e-akram hospital, iran university of medical sciences, tehran, iran. mohammad nabavi department of allergy and clinical immunology, rasool-e-akram hospital, iran university of medical sciences, tehran, iran. tatjana hirschmugl cemm research center for molecular medicine, austrian academy of sciences, vienna, austria. asghar aghamohammadi research center for immunodeficiencies, children's medical center, tehran university of medical sciences, tehran, iran. saba arshi department of allergy and clinical immunology, rasool-e-akram hospital, iran university of medical sciences, tehran, iran. mohamad hassan bemanian department of allergy and clinical immunology, rasool-e-akram hospital, iran university of medical sciences, tehran, iran.

lps-responsive beige-like anchor (lrba) deficiency is a disease which has recently been described in a group of patients with common variable immunodeficiency (cvid) in association with autoimmunity and/or inflammatory bowel disease (ibd)-like phenotype. we here describe a 10-year-old boy who experienced recurrent infections, mainly in the respiratory system, associated with thrombocytopenia an...

Journal: :Molecular syndromology 2013
B D Solomon D E Pineda-Alvarez D W Hadley N F Hansen A Kamat F X Donovan S C Chandrasekharappa S-K Hong E Roessler J C Mullikin

Exome sequencing offers an efficient and affordable method to interrogate genetic factors involved in human disease. Performing exome sequencing of monozygotic twins discordant for VACTERL (Vertebral anomalies, Anal atresia, Cardiac malformations, Tracheo-Esophageal fistula, Renal anomalies, and Limb abnormalities) association-type congenital malformations was hypothesized to potentially reveal...

Journal: :JAMA 2014
Yaping Yang Donna M Muzny Fan Xia Zhiyv Niu Richard Person Yan Ding Patricia Ward Alicia Braxton Min Wang Christian Buhay Narayanan Veeraraghavan Alicia Hawes Theodore Chiang Magalie Leduc Joke Beuten Jing Zhang Weimin He Jennifer Scull Alecia Willis Megan Landsverk William J Craigen Mir Reza Bekheirnia Asbjorg Stray-Pedersen Pengfei Liu Shu Wen Wendy Alcaraz Hong Cui Magdalena Walkiewicz Jeffrey Reid Matthew Bainbridge Ankita Patel Eric Boerwinkle Arthur L Beaudet James R Lupski Sharon E Plon Richard A Gibbs Christine M Eng

IMPORTANCE Clinical whole-exome sequencing is increasingly used for diagnostic evaluation of patients with suspected genetic disorders. OBJECTIVE To perform clinical whole-exome sequencing and report (1) the rate of molecular diagnosis among phenotypic groups, (2) the spectrum of genetic alterations contributing to disease, and (3) the prevalence of medically actionable incidental findings su...

Journal: :The New England journal of medicine 2014
Jan Westerink Frank L J Visseren Wilko Spiering

From the National Human Genome Research Institute, National Institutes of Health, Bethesda, MD (L.G.B.); and the Division of Genetics, Department of Medicine, Brigham and Women’s Hospital and Harvard Medical School, and Partners Healthcare Personalized Medicine — all in Boston (R.C.G.). Address reprint requests to Dr. Biesecker at 49 Convent Dr., Rm. 4A56, Bethesda, MD 20892-4472, or at lesb@ma...

Journal: :iranian red crescent medical journal 0
hadi shirzad department of medical genetics, faculty of medical sciences, tarbiat modares university, tehran, ir iran narges beiraghi department of psychology, faculty of psychology, shahid beheshti university of medical sciences, tehran, ir iran mojgan ataei kachoui tehran medical genetics laboratory, tehran, ir iran mohammad taghi akbari department of medical genetics, faculty of medical sciences, tarbiat modares university, tehran, ir iran; tehran medical genetics laboratory, tehran, ir iran; department of medical genetics, faculty of medical sciences, tarbiat modares university, tehran, ir iran. tel: +98-2182884517

conclusions by applying wes, both novel and known scz pathogenic variants with complete or incomplete segregation in the families with multiple cases of schizophrenic patients were identified. background schizophrenia (scz) is a complex neuropsychiatric disorder characterized by pronounced genetic heterogeneity. much of the genetic architecture of the disorder has not yet been clearly elucidate...

Journal: :genetics in the 3rd millennium 0
mojgan babanejad mohammad reza akbari nooshin nikzat1 sanaz arzhangi hossein najmabadi kimia kahrizi

introduction: with prevalence figures close to 0.2% at birth, hearing loss (hl) is the most frequent sensory impairment in childhood. in developed countries, genetic causes account for more than 60% of congenital hl, most often resulting in non-syndromic deafness, which is usually autosomal recessive. hereditary nonsyndromic hearing loss (nshl) in iran is highly heterogeneous, rendering molecul...

2012
Karthik Kota David Jenkins John Seed Justin Johnson

Journal: :Neurology. Clinical practice 2016
Brent L Fogel Saty Satya-Murti Bruce H Cohen

PURPOSE OF REVIEW The landscape of genetic diagnostic testing has changed dramatically with the introduction of next-generation clinical exome sequencing (CES), which provides an unbiased analysis of all protein-coding sequences in the roughly 21,000 genes in the human genome. Use of this testing, however, is currently limited in clinical neurologic practice by the lack of a framework for appro...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید