Churg-Strauss syndrome is a rare diffuse small/medium sized vessel vasculitis that is almost invariably accompanied by severe asthma. The cause is unknown, but its characteristic histological findings and association with asthma distinguish it from other vasculitides. We report here a middle aged lady who presented with sudden onset of vasculitic skin lesions in association with long standing a...

PURPOSE Retinal vascular abnormalities are rare in patients with Churg-Strauss syndrome. We present the findings in a patient with Churg-Strauss syndrome who developed bilateral central retinal artery occlusion simultaneously. METHODS Case report. RESULTS A 68-year-old Japanese man developed acute bilateral vision decrease to counting finger in the right eye and hand movements in the left e...

We report on a case of Churg-Strauss syndrome in a 30 year old male with a history of perennial rhinitis. The syndrome began nine months earlier with clinico-radiological features typical of chronic eosinophilic pneumonia. Diagnosis of vasculitis was made by skin biopsy, and at that time there was multisystemic involvement with pulmonary, cardiac, renal, cutaneous and muscular disease, and righ...

Adjuvant medical treatment steroid therapy of polyarteritis nodosa. Specific treatments are sometimes required. 55: 146–155 renal vasculitis. Angiotensin converting enzyme inhib-10. Guillevin L, Jarrousse B, Lok C et al. Long-term followup after itors or angiotensin II-receptor blockers are effective treatment of polyarteritis nodosa and Churg–Strauss angiitis and able to control severe or mali...

First described in 1951 as an allergic and granulomatous angiitis, Churg-Strauss syndrome (CSS) is a small-vessel vasculitis. Mean age at the time of diagnosis is approximately 50 years, with a sex ratio around 1. Asthma is the central feature of CSS and precedes the systemic manifestations in almost all cases, whereas 70% of the patients have maxillary sinusitis, allergic rhinitis, and/or sinu...

Pulmonary: asthma, pneumonitis and haemoptysis. Upper respiratory tract: allergic rhinitis, paranasal sinusitis, nasal polyposis. Cardiac involvement is common. [6]This includes heart failure, myocarditis and myocardial infarction. [7] Skin: purpura, skin nodules, leukocytoclastic angiitis with palpable purpura, livedo reticularis, urticaria, necrotic bullae and digital ischaemia. Renal: glomer...

A 44 year old female nurse with a 20-year history of severe, steroid-dependent asthma, hypertension, hematuria, pleuritis, and sinusitis was referred from her ophthalmologist in January 2000, with the question of possible bilateral scleritis. The patient was treated with topical steroid (prednisolone acetate 6 times daily) for anterior uveitis, systemic prednisone (50mg per os) and steroid inha...

Churg Strauss syndrome is a rare systemic and pulmonary vasculitis exceptionally associated with AA amyloidosis. We report the case of a 65-year old woman with past medical history of asthma. She developed polyarthralgia, headache and purpura. A laboratory workout found hypereosinophilia (1150/µL), positive p-ANCA, microscopic haematuria and proteinuria at 2g/day. A diagnosis of Churg-Strauss s...