the majority of coronary artery fistulas (cafs) are congenital. the anomaly accounts for 0.4% of congenital heart defects and approximately 50% of pediatric coronary vasculature anomalies. twenty percent of people with congenital cafs have other concomitant cardiac anomalies, most frequently aortic and pulmonary atresia and patent ductus arteriosus. it is worthy of note that caf with the tetral...

OBJECTIVES To assess clinical presentation, treatment, and outcome of children with Ebstein's anomaly. BACKGROUND Data on long-term outcome of children with Ebstein's anomaly are scarce. METHODS Retrospective analysis of all children with Ebstein's anomaly treated between February, 1979 and January, 2009 in a single tertiary institution. Primary outcomes included patient survival and need f...

epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. multicystic kidney disease has been very rarely reported in this syndrome. here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with wilms' tumor. according to this ...

Four cases of Ebstein's anomaly are described, revealing that the clinical features permit diagnosis in the majority of instances and that cardiac catheterization affords precise confirmation of the diagnosis. The occurrence of this anomaly in acyanotic adults is pointed out. and the similarity to acquire(I valvular rheumatic heart disease is stressed. r 'HE congenital cardiac defect known as E...

Ebstein's anomaly of the tricuspid valve is a rare lesion comprising less than 1% of patients with congenital heart disease. Among congenital heart lesions, Ebstein's anomaly is one of the most diverse in presentation, severity, and management. In its most severe form, it is also one of the most lethal. In this article we present a case of a patient who developed cardiac symptoms in adulthood. ...

Introduction: Since 1954, after the first surgical repair of tetralogy of Fallot (TOF), several innovations have occurred in cardiac surgery, especially in children. One stage complete repair of TOF is currently possible even in infancy; however, complications such as hypoxemia, arrhythmia, cardiac dysfunction, sudden death, and valvular disorders may happen. In this study, we evaluated the res...

congenital absence of left circumflex artery is a rare congenital anomaly of the coronary arteries. the prevalence of the anomaly in different studies ranges from 0.6% to 1.3%. of these, 80% are benign and asymptomatic and 20% are clinically important. we report a 56-year-old man presented with acute resting chest pain who was diagnosed as having acute anterolateral infarction accompanied by el...