IgG4-related disease is a new disease entity involving IgG4 in its clinical presentation and having 6 characteristic features: (1) systemic involvement; (2) solitary or multiple lesions showing diffuse or localized swelling, masses, nodules, and/or wall thickening on imaging; (3) high serum IgG4 concentration >135 mg/dL; (4) abundant infiltration of lymphoplasmacytes and IgG4-bearing plasma cel...

PURPOSE Autoimmune pancreatitis is a unique form of chronic pancreatitis characterized by a variety of extra-pancreatic involvements which are frequently misdiagnosed as lesions of corresponding organs. The purpose of this study was to clarify the diagnostic imaging features of extra-pancreatic lesions associated with autoimmune pancreatitis. MATERIALS AND METHODS We retrospectively analyzed ...

CONTEXT A case of autoimmune pancreatitis develops a hepatic metastasis of bladder cancer resected over 5 years before, mimicking a pseudotumor of the liver. CASE REPORT A 71-year-old man with a surgical history of bladder cancer (pT4, G2>3, N (+)) later developed autoimmune pancreatitis. Diagnosis of autoimmune pancreatitis was not problematic; however, a variety of systemic disorders app...

OBJECTIVE The purpose of this article is to discuss the systemic nature of autoimmune pancreatitis and its various pancreatic and extrapancreatic imaging findings. CONCLUSION Autoimmune pancreatitis is a systemic disease with a wide range of pancreatic and extrapancreatic imaging findings. These findings can mimic those of other diseases in the pancreas or other organs and therefore are commo...

Autoimmune pancreatitis (AIP) is a rare and underdiagnosed fibrosclerosing inflammatory variant of chronic pancreatitis. Its true incidence and prevalence in the general population is still not confirmed despite advances in medicine. Differentiating it from pancreatic cancer is of paramount importance. In this imaging review, we highlight the imaging findings of this intriguing entity.

CONTEXT Autoimmune pancreatitis is increasingly being diagnosed as a multiorgan disorder and a small group of patient present a diagnostic and management dilemma. CASE REPORT We report a complicated case of autoimmune pancreatitis with multiorgan involvement. This is the first reported case of pericardial involvement and agrees with other authors that autoimmune pancreatitis is a multisystem ...

CONTEXT Autoimmune pancreatitis is a rare disorder characterized by the systemic deposition of IgG4 plasma cells. Extrapancreatic manifestations of autoimmune pancreatitis depend on the site of plasma cell deposition. The most common extrapancreatic site of involvement is the bile duct followed by the retroperitoneum and kidneys. CASE REPORT We report a case of a patient with autoimmune pancr...

The association between autoimmune pancreatitis and sclerosing cholangitis has attracted considerable attention. In contrast to type 1 (IgG4-related) autoimmune pancreatitis, bile duct involvement is uncommon in type 2 autoimmune pancreatitis, a more benign condition characterized histologically by granulocytic epithelial lesions (GELs). Following our recent report on a child with GEL-positive ...

CONTEXT Autoimmune pancreatitis is a rare benign disorder that can be confused with pancreatic cancer and the treatment pathway differs dramatically. CASE REPORT We present a unique case of pulmonary nodules associated with autoimmune pancreatitis, that was initially confused for pancreatic cancer which resolved spontaneously. Herein we describe the case and subsequent management and discuss ...

Over the past two decades, the quality of diagnostic imaging in the pancreas has been improved by technical and instrumental progress made in ultrasonography (US), computed tomography (CT) and magnetic resonance imaging (MRI). The examination using ultrasound is inexpensive, non-invasive, and can be rapidly performed. It is often the test of choice in the evaluation of suspected pancreatic lesi...