Spinal muscular atrophy (SMA), an autosomal recessive disease, is characterized by the selective loss of spinal motor neurons due to reduced levels of the survival motor neuron (SMN) protein. The clinical symptoms of SMA are progressive proximal muscle weakness and paralysis. Here we describe a 20-year-old Turkmenistan male with SMA who presented with uncommon pathological reflexes and asymmetr...

the pseudo-elastic behavior of shape memory alloy (sma) truss and cantilever beam are investigated. brinson’s one-dimensional material model, which uses the twinned and detwinned martensite fractions separately as internal variables, is applied in the algorithm to establish the sma stress-strain characteristics. this material model also incorporates different young’s modulus for austenitic and ...

Irregularities in bridge pier stiffness concentrate the ductility demand on short piers; while not operating on the longer and more flexible ones. The existence of non-uniform, ductility demand distribution in bridges significantly influences seismic response. As such, this paper proposes a new approach for balancing the ductility demand in irregular bridges by utilizing shape memory alloys (SM...

Several series of novel banana-shaped H-bonded symmetric trimers (with two H-bonds) and asymmetric heterodimers (with one H-bond) were self-assembled by appropriate molar ratios of proton donors (H-donors) and acceptors (H-acceptors). The influences of H-bonded linking positions and aromatic ring numbers (4-8 aromatic rings in the rigid cores) as well as the chain lengths (n, m = 12 or 16, resp...

Concentrically braced frames (CBFs) are one of the efficient lateral load resisting systems in high seismicity regions. One of the common problems with the use of concentrically braced frames is limitation in the architectural application and position of the openings. Two-story X braced frames have more advantages than other configurations of concentrically braced frames, since in many cases th...