An 11-year-old girl and a known case of tuberous sclerosis was referred for ophthalmic evaluation. The parents had noted multiple pigmented lesions on her face, scalp and neck since the age of 3 years. There were no neurological symptoms at the time of presentation. General physical examination revealed adenoma sebaceum on her face (Figure 1A), neck (Figure 1C) and scalp; a shagreen patch was d...

Neurofibromatosis type 2 (NF-2) is characterized by multifocal proliferation of neural crest-derived cells. The characteristics finding of NF-2 is bilateral vestibular schwannomas. Combined hamartoma of retina and retinal epithelium (CHRRPE) is another associated finding. A 9 year-old-male child presented with left eye decreased vision for 3 months. Visual acuity was 0.0 and 0.8 LogMAR in the r...

While pediatric orbital tumors are most often managed in tertiary care centers, clinicians should be aware of the signs of intraocular and orbital neoplasms. In the pediatric population, a delay in diagnosis of orbital and intraocular lesions, even if benign, can lead to vision loss and deformity. Intraocular lesions reviewed are retinoblastoma, medulloepithelioma, and retinal astrocytic hamart...

Hamartoma is a local malformation resulting from faulty development in an organ. It was first described breast 1971 by Arrigoni et al and its occurrence very rare. This tumor composed of lobules admixed with fibrous tissue fibroadipose tissue. Myoid hamartoma, also called as muscular hamartoma , smooth muscle cells addition to ducts, lobules, stroma. Here, we report case myoid which occurred 53...

: Hydatid cyst is one of the predominantly cystic liver lesions and also a zoonotic disease that highly endemic in Mediterranean region. This condition has extensive differential diagnoses, such as hepatic mesenchymal hamartoma, rare benign tumor, which commonly occurs infants children, extremely adults. Its imaging findings vary from tumor to solid mass occupying or both lobes liver. We report...

Hamartoma es una masa desorganizada, benigna, compuesta por tejidos y células nativas de sitio anatómico afectado. El hamartoma lingual infantil un tumor benigno e infrecuente que generalmente se descubre en la niñez. No conoce patogenia, pero parece estar relacionada a persistencia restos embrionarios mesenquimales. Se presenta el caso paciente con patología región lingual.

Nasal chondromesenchymal hamartoma has characteristic clinicopathological features and it is accepted as the upper airway analogue of mesenchymal hamartoma of the chest wall. It is a rare lesion and only 31 cases have been reported in the English literature until 2014. In this article, a 13-year-old nasal chondromesenchymal hamartoma case is presented, which is the first nasal chondromesenchyma...

splenic hamartoma is an unusual accidental finding with non-neoplastic feature that may be incidentally diagnosed because of its compression effect on surrounding organs. the predominant pathological feature leading diagnosis is circumscribed, un-encapsulated bulging nodules with focal fibrosis or cyst. the histopathological feature of splenic hamartoma is the positivity for cd8, and occasional...