Normal/increased pressure hydrocephaly is an unusual manifestation of systemic lupus erythematosus (SLE), and the pathogenesis is still unclear. We report the case of an 18-year-old white female with severe refractory renal and pulmonary involvement who developed stupor during intensive immunosuppressive treatment. Enlarged ventricles on imaging and increased intracranial pressure with the excl...

Objective Arteriovenous malformation (AVM) is the most common form of intracranial vascular malformations in adults. Intracranial pediatric AVMs are rare. AVM located in the vicinity of the brain stem in children are even more rare. Case report This study reports a rare case of acute obstructive hydrocephalus following aqueductal stenosis caused by an unruptured grade IV perimesencephalic art...

Klinefelter's syndrome is a frequent genetic sexual alteration in males, associated with the 47,XXY aneuploidy. Several syndrome variants are caused by different X and Y polysomy and mosaicisms, including the 49,XXXXY condition described by some authors as Fraccaro's syndrome. Mosaics with three or more different chromosomal lines are very rare. Here, we describe a case with XXY/XXXY/XXXXY mosa...

The objectives of the present study were to describe pathomorphological and immunohistochemical features of congenital cerebellar hypoplasia associated with natural BVD-MD virus infection in a Holstein-Friesian calf. The characteristic macroscopical lesion was cerebellar hypoplasia, almost completely absent, with hydrocephaly. Cerebellar changes were cortical destruction, destructive changes of...

Anomalies related to cardiovascular system are the most commonly seen congenital anomalies that are the causes of death during the newborn period. Central nervous systems anomalies such as; microcephaly, anencephaly, hydrocephaly, encephalosel, spina bifida are also well defined as the frequent causes of death [1]. The aim of this study is to present an infantile postpartum death case, caused b...

We present a case with frontal lobe symptoms and Klüver-Bucy-like syndrome following subarachnoid hemorrhage and hydrocephaly. Klüver-Bucy syndrome is a rare neurobehavioral condition characterized by placidity, visual agnosia, hypersexuality, hyperorality, and hypermetamorphosis (the tendency to react to or to touch every visual stimulus). The syndrome is usually associated with lesions of the...