نتایج جستجو برای: urbach wiethe disease

تعداد نتایج: 1490423  

Journal: :Neuropsychologia 2007
René Hurlemann Michael Wagner Barbara Hawellek Harald Reich Peter Pieperhoff Katrin Amunts Ana-Maria Oros-Peusquens Nadim J Shah Wolfgang Maier Raymond J Dolan

When presented in a neutral context, emotional items interfere with episodic encoding of temporally contiguous non-emotional items, resulting in dissociable valence-dependent retrograde and arousal-dependent anterograde modulatory effects. By studying two rare patients with congenital lipoid proteinosis (Urbach-Wiethe) and a focal disease emphasis on the basolateral amygdala (BLA), we demonstra...

Journal: :JPMA. The Journal of the Pakistan Medical Association 1996
Z H Hafeez T Hussain

Journal: :Social cognitive and affective neuroscience 2009
René Hurlemann Thomas E Schlaepfer Andreas Matusch Harald Reich Nadim J Shah Karl Zilles Wolfgang Maier Andreas Bauer

Neurobiological evidence implicates the amygdala as well as serotonergic (serotonin, 5-HT) signaling via postsynaptic 5-HT(2A) receptors as essential substrates of anxiety behaviors. Assuming a functional interdependence of these substrates, we hypothesized that a low-fear behavioral phenotype due to bilateral lesion of the amygdala would be associated with significant 5-HT(2A) receptor changes...

Journal: :Brain : a journal of neurology 2003
Michaela Siebert Hans J Markowitsch Peter Bartel

Patients with Urbach-Wiethe disease constitute a unique nature experiment as more than half have bilaterally symmetrical damage in the amygdaloid region. Ten such patients were studied neuropsychologically and, nine of them, neuroradiologically with static (CT) and functional imaging techniques [single-photon emission computed tomography (SPECT) and PET]. Their principal bilateral amygdala dama...

Journal: :گوارش 0
hosein ajdarkosh samira shirzad mohammad taher naser ebrahimidaryani farhad zamani

lipoid proteinosis (lp) is a rare autosomal recessive disease characterized by the deposition of an amorphous hyaline material in the skin, mucosa and viscera. the classic manifestation is onset in infancy with a hoarse cry due to laryngeal infiltration. skin and mucous changes develope, and the disease follows a slowly progressive course. in this case report, a 49 year-old man presented with a...

Journal: :Proceedings of the Royal Society of Medicine 1961

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