Isolated unilateral absence of pulmonary artery (UAPA) is a rare congenital anomaly. When detected in infancy, the condition is commonly associated with cardiovascular defects which are more frequently associated with left pulmonary artery agenesis. Patients with isolated right pulmonary artery agenesis survive into adulthood with minimal or no symptoms and are diagnosed incidentally on the che...

We are reporting here, a case of an incidentally detected, isolated, unilateral pulmonary artery agenesis on contrast enhanced Computed Tomography (CT) of the chest in a 39-year-old male patient.

A twenty-three-year-old male truck driver with a 12-pack year smoking history and no previous of hospitalization was admitted to the “Shefqet Ndroqi” University Hospital pulmonology department after cardiologist consultation where he diagnosed pulmonary hypertension. Two patient’s uncles from his mother’s side died during their pediatric age congenital heart defects. contrast-enhanced chest com...

BACKGROUND Unilateral pulmonary artery agenesis (UPAA) is a rare congenital anomaly due to a malformation of the sixth aortic arch of the affected side during embryogenesis. The diagnosis is usually set at adolescence, however it can remain asymptomatic and late diagnosis is possible. DESCRIPTION We present a case series of three female patients, aged 18, 49 and 68 years old, with history of ...